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. 2025 Jan 27;3(1):e001047. doi: 10.1136/bmjph-2024-001047

Table 3. Annual incidence of systemic amyloidosis in different regions.

Authors and year Country Period Annual incidence
Posadas-Martínez et al, current study Argentina 2011–2022 ATTRwt amyloidosis (over 60 years): 66/1 000 000 person–yearsAL amyloidosis: 16/1 000 000 person–yearsAA amyloidosis: 4/1 000 000 person–years
Kyle et al, 1992 USA 1950–1989 AL amyloidosis: 6.0 to 10.5/1 000 000 person–years6
Laires et al, 202315 USA AL amyloidosis: 16.7/1 000 000 person–years15
Cappelli et al, 202316 Italy 2006–2022
  • ATTRwt amyloidosis: 14.4 to 26.7/1 000 000 person–years.16

  • ATTRv amyloidosis: 0.8 to 2.7/1 000 000 person–years.

Mellqvist et al, 202317 Swedish 2011–2019 AL amyloidosis: 10.5 to 15.1/1 000 000 person-years17
Dammy et al, 202318 France 2011–2019 ATTR-CA: 0.6 to 3.6/100 000 person-years18
Hemminki et al, 20128 Swedish 2001–2008
  • All types: 8.29/1 000 000 person-years.

  • Secondary systemic amyloidosis: 1.18/1 000 000 person-years8

Pinney et al, 20137 UK 2000–2008
  • All types: 0.2 to 0.4/100 000 person-years

  • AL amyloidosis: 0.3 to 0.3/100 000 person-years7

Laires et al, 202419 USA 2018–2022 ATTR-CA: 6/1 000 000 person-years19
Gilstrap et al, 201920 USA 2000–2012 ATTR-CA: 1.8 to 5.5/1 000 000 person-years20
Guha et al, 202421 UK 2004–2021 ATTR-CA: 0.7–1.96/100 000 person-years21
Choi et al, 202422 Korea 2008–2020 ATTR-CA: 0.09–0.22/100 000 person-years22
Quock et al, 201814 USA 2007–2015 Amyloidosis AL: 9.7 to 14.0/1 000 000 person-years14 22
Brink et al Netherlands 2017–2018 Amyloidosis AL: 6.0/1 000 000 person-years