| AD | Alzheimer’s disease |
| PD | Parkinson’s disease |
| HD | Huntington’s disease |
| ALS | amyotrophic lateral sclerosis |
| Aβ | amyloid-β |
| MPTP | 1-methyl-4-phenyl-1,2,3,6-tetrahydropyridine |
| ETC | electron transport chain |
| ROS | reactive oxygen species |
| mtDNA | mitochondrial DNA |
| ER | endoplasmic reticulum |
| MAMs | mitochondria-associated membranes |
| OMM | outer mitochondrial membrane |
| IMM | inner mitochondrial membrane |
| IMS | intermembrane Space |
| OXPHOS | oxidative phosphorylation |
| NADH | nicotinamide adenine dinucleotide |
| FADH2 | flavian adenine dinucleotide |
| ATP | adenosine triphosphate |
| ADP | adenosine diphosphate |
| Mfn1/2 | MItofusin 1/2 |
| OPA1 | optic atrophy 1 |
| Drp1 | dynamin-related protein 1 |
| Fis1 | fission1 |
| Mff | mitochondrial fission factor |
| MiD49 | mitochondrial dynamics protein 49 |
| MCU | mitochondrial calcium uniporter |
| mPTP | mitochondrial permeability transition pore |
| NCLX | Na+/Ca2+ exchanger |
| UPS | Uniquitin-proteasome System |
| MDVs | Mitochondrial-derived Vesicles |
| PINK1 | PTEN-induced Kinase 1 |
| SQSTM1 | Sequestosome 1 |
| NBR1 | neighbor of BRCA1 gene |
| OPTN | optineurin |
| BNIP3 | Bcl-2/adenovirus E1B 19 kDa-interacting protein 3 |
| FUNDC1 | FUN14 domain-containing 1 |
| SOD | Superoxide Dismutase |
| ABAD | amyloid-beta-binding alcohol dehydrogenase |
| TDP-43 | TAR DNA-binding protein-43 |
| DAMPs | damage-associated molecular patterns |
| FUS | fused in sarcoma |
| PGC-1α | peroxisome proliferator-activated receptor gamma coactivator 1-alpha |
| fAD | familial AD |
| APP | amyloid precursor protein |
| PSEN | presenilin |
| sAD | sporadic AD |
| APOE | apolipoprotein E |
| LRRK2 | leucine-rich repeat kinase 2 |
| SNCA | α-synuclein |
| fALS/sALS | familial/sporadic ALS |
| NAD | nicotinamide adenine dinucleotide |
| SIRT1 | sirtuin 1 |
| NAM | nicotinamide |
| USP30 | ubiquitin-specific Peptidase 30 |
| DCA | dichloroacetate |
| BBB | blood–brain barrier |
| CSF | cerebrospinal fluid |
| 8-OHdG | 8-hydroxy-2′-deoxyguanosine |
| FGF21 | fibroblast growth factor 21 |
| GDF15 | growth differentiation factor 15 |
| PET | Positron Emission Tomography |
| CRISPR/Cas9 | clustered regularly interspaced short palindromic repeats/CRISPR-associated protein 9 |
| iPSC | induced pluripotent stem cell |
| UPRmt | mitochondrial unfolded protein response |