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. Author manuscript; available in PMC: 2025 Feb 26.
Published in final edited form as: Nat Med. 2024 Jun 17;30(9):2517–2527. doi: 10.1038/s41591-024-03076-6

Table 3.

Efficacy by Disease Subtype.

Histology Arm A Arm B
Romidepsin + Duvelisib Bortezomib + Duvelisib
All Patients at MTD only All Patients at MTD only
Evaluable ORR CRR PRR Evaluable ORR CRR PRR Evaluable ORR CRR PRR Evaluable ORR CRR PRR
n % (n) % (n) % (n) n % (n) % (n) % (n) n % (n) % (n) % (n) n % (n) % (n) % (n)
Peripheral T-cell Lymphoma 53 58 (31) 42 (22) 17 (9) 48 56 (27) 44 (21) 13 (6) 16 44 (7) 25 (4) 19 (3) 12 42 (5) 17 (2) 25 (3)
 PTCL-NOS 18 50 (9) 28 (5) 22 (4) 17 47 (8) 29 (5) 18 (3) 7 57 (4) 29 (2) 29 (2) 6 50 (3) 17 (1) 33 (2)
 AITL/PTCL-TFH 20 70 (14) 60 (12) 10 (2) 17 71 (12) 65 (11) 6 (1) 4 75 (3) 50 (2) 25 (1) 2 100 (2) 50 (1) 50 (1)
 ALCL 3 100 (3) 67 (2) 33 (1) 3 100 (3) 67 (2) 33 (1) 2 0 - - 1 0 - -
 pcGDTCL 3 33 (1) 33 (1) - 3 33 (1) 33 (1) - - - - - - - -
 HSTCL 2 50 (1) - 50 (1) 1 0 - - - - - - - - -
 MEITL 1 0 - - 1 0 - - - - - - - - -
 Aggressive Epidermotropic CD8+ TCL 2 50 (1) 50 (1) - 2 50 (1) 50 (1) - - - - - - - -
 Other 4 50 (2) 25 (1) 25 (1) 4 50 (2) 25 (1) 25 (1) 3 0 - - 3 0 - -
  T-PLL 1 0 - - 1 0 - - 1 0 - - 1 0 - -
  ATLL 1 0 - - 1 0 - - 1 0 - - 1 0 - -
  pcPTCL 1 100 (1) - 100 (1) 1 100 (1) - 100 (1) - - - - - - - -
  PTLD 1 100 (1) 100 (1) - 1 100 (1) 100 (1) - - - - - - - - -
  ENNK/TCL 0 - - - 0 - - - 1 0 - - 1 0 - -
Cutaneous T-cell Lymphoma 11 36 (4) 0 36 (4) 9 44 (4) 0 44 (4) 16 25 (4) 0 25 (4) 11 18 (2) 0 18 (2)
 MF 7 29 (2) - 29 (2) 5 40 (2) - 40 (2) 9 11 (1) - 11 (1) 7 14 (1) - 14 (1)
  - Transformed 3 0 - - 1 0 - - 4 0 - 2 0 - -
 SS 4 50 (2) - 50 (2) 4 50 (2) - 50 (2) 7 43 (3) - 43 (3) 4 25 (1) - 25 (1)
  - Transformed 1 0 - 1 0 - - 2 0 - 2 0 - -
TOTAL 64 55 (35) 34 (22) 20 (13) 57 54 (31) 37 (21) 18 (10) 32 34 (11) 13 (4) 22 (7) 23 30 (7) 9 (2) 22 (5)

PTCL-NOS, peripheral T-cell lymphoma not otherwise specified; AITL, angioimmunoblastic T-cell lymphoma, Tfh, T-follicular helper; ALCL, anaplastic large cell lymphoma; pcGDTCL, primary cutaneous gamma-delta T-cell lymphoma; HSTCL, hepatosplenic T-cell lymphoma; MEITL, monomorphic epitheliotrophic intestinal T-cell lymphoma; T-PLL, T-prolymphocytic leukemia; ATLL, acute T-cell leukemia/lymphoma; PTLD, peripheral T-cell lymphoproliferative disorder; EN-NK/TCL, extranodal natural killer/T-cell lymphoma; MF, mycosis fungoides; SS, Sezary syndrome.