TABLE 1.
Clinical data of patients in the CHZ‐01 family.
| Subject | Gender | Age of test (years) | Age of onset (years) | Better ear | ||
|---|---|---|---|---|---|---|
| PTA (dB HL) | Hearing loss | Associated symptoms | ||||
| II:3 | Male | 63 | 25 | 71.25 | Severe | Not |
| II:5 | Male | 58 | 25 | 72.5 | Severe | Not |
| II:8 | Male | 54 | 11 | 66.25 | Severe | Tinnitus |
| III:3 | Female | 35 | 11 | 57.5 | Moderately severe | Not |
| III:9 | Male | 35 | 17 | 52.5 | Moderately severe | Tinnitus |
| IV:3 | Male | 11 | 8 | 50 | Moderate | Not |
Note: PTA, pure‐tone air‐conduction averages (0.5, 1, 2, and 4 kHz) for the better hearing ear of affected subjects in family CHZ‐01.