hGFBs |
human TERT-immortalized gingival fibroblasts |
mhGFBs |
heterozygous C1RR301P/WT-mutated hGFBs |
MMP-1 |
matrix metalloproteinase-1 |
IL-6 |
interleukin-6 |
TIMP-1 |
tissue inhibitor of metalloproteinase-1 |
C1r (C1R) |
complement component 1r (1R) |
C1s (C1S) |
complement component 1r (1S) |
CD90 |
cluster of differentiation 90 |
Col1α1 |
procollagen α1(I) |
Col3 α1 |
procollagen α1(III) |
Col5 α1 |
procollagen α1(V) |
pEDS |
periodontal Ehlers–Danlos syndrome |
FB |
fibroblast |
ICC |
immunocytochemical staining |
PDT |
population doubling time |
PDGFRα |
platelet-derived growth factor receptor alpha |
TNF-α |
tumor necrosis factor alpha |
IL-1β |
interleukin-1 beta |
pegRNA |
prime editing guide RNA |
PCR |
polymerase chain reaction |
ddPCR |
droplet digital PCR |
MTT |
3-(4,5-dimethylthiazol-2-yl)-2,5-diphenyltetrazolium bromide |
F-CHP |
fluorescence-collagen hybridizing peptide |
DAPI |
4′6′-Diamidino-2-phenylindole dihydrochloride |
ELISA |
enzyme-like immunosorbent assay |
RT-qPCR |
real-time quantitative reverse transcription polymerase chain reaction |
RPLP0 |
ribosomal protein lateral stalk subunit P0 |
RNA |
ribonucleic acid |
mRNA |
message RNA |
ECM |
extracellular matrix |
ER |
endoplasmic reticulum |