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. 2025 Mar 22;14(7):479. doi: 10.3390/cells14070479
hGFBs human TERT-immortalized gingival fibroblasts
mhGFBs heterozygous C1RR301P/WT-mutated hGFBs
MMP-1 matrix metalloproteinase-1
IL-6 interleukin-6
TIMP-1 tissue inhibitor of metalloproteinase-1
C1r (C1R) complement component 1r (1R)
C1s (C1S) complement component 1r (1S)
CD90 cluster of differentiation 90
Col1α1 procollagen α1(I)
Col3 α1 procollagen α1(III)
Col5 α1 procollagen α1(V)
pEDS periodontal Ehlers–Danlos syndrome
FB fibroblast
ICC immunocytochemical staining
PDT population doubling time
PDGFRα platelet-derived growth factor receptor alpha
TNF-α tumor necrosis factor alpha
IL-1β interleukin-1 beta
pegRNA prime editing guide RNA
PCR polymerase chain reaction
ddPCR droplet digital PCR
MTT 3-(4,5-dimethylthiazol-2-yl)-2,5-diphenyltetrazolium bromide
F-CHP fluorescence-collagen hybridizing peptide
DAPI 4′6′-Diamidino-2-phenylindole dihydrochloride
ELISA enzyme-like immunosorbent assay
RT-qPCR real-time quantitative reverse transcription polymerase chain reaction
RPLP0 ribosomal protein lateral stalk subunit P0
RNA ribonucleic acid
mRNA message RNA
ECM extracellular matrix
ER endoplasmic reticulum