Table 1.
Epithelioid malignant peripheral nerve sheath tumors
| Author | Year | Age | Sex | Location | Size, cm | NF1 | SMARCB1/INI-I | Treatment | Outcome |
|---|---|---|---|---|---|---|---|---|---|
| Lee | 1997 [6] | 63 | F | Vulva | 6 × 4 × 1.5 | No | NA | Resection | Alive |
| Ikebe | 2010 [5] | 82 | F | Axilla | 10 × 10 | No | NA | Resection | Alive |
| Minagawa | 2011 [8] | 62 | M | Foot | 7 × 4.3 | No | NA | Resection+chemotherapy*1 | Alive |
| Carter | 2012 [17] | 31 | F | Leg | 6.7 | No | Absent | Resection | NA |
| Atsumi | 2014 [3] | 60 | M | Transverse colon | 14.5 × 6.6 | Yes | NA | Transverse colon resection | Dead |
| Kusumoto | 2015 [14] | 70 | M | Axilla | 21 × 17 × 8 | No | NA | Resection | Dead |
| Gupta | 2017 [9] | 40 | M | Flank | 9.7 × 7.5 | Yes | NA | None | Dead |
| Du | 2019 [12] | 71 | F | Lower back | 20 × 13 × 8 | Yes | NA | Resection+radiotherapy | Alive |
| Patra | 2019 [16] | 65 | M | Rectum | 5.5 × 3.5 × 3.5 cm | No | Retained | Resection | Alive |
| Patra | 2019 [16] | 47 | F | Rectum | 5 cm | No | Retained | Polypectomy, radiotherapy | Dead |
| Matsumoto | 2020 [4] | 49 | F | Rectum | 30 × 25 × 25 | Yes | NA | Posterior pelvic exenteration | Dead |
| Zhang | 2020 [7] | 16 | F | Lung | 4 × 4 × 3 | No | NA | Lobectomy | Dead |
| Heatley | 2020 [18] | 25 | F | Thigh | 2.1 × 1.1 × 1.1 | No | Absent | Resection | Alive |
| Guzin | 2021 [10] | 56 | F | Vagina | 3 × 2 × 2.5 | No | NA | Resection | Alive |
| Biglow | 2021 [15] | 47 | F | Finger | 0.8 × 0.5 × 0.8 | No | Absent | Resection | Alive |
| Treeck | 2022 [13] | 20 | F | Liver | 11 cm | No | Absent | NA | NA |
| Qi | 2023 [11] | 3 | M | Lumbar 5, sacral 1 | 4.2 × 3 × 2.1 cm | No | Absent | Resection+chemotherapy*2+radiotherapy | Alive |
| Our case | 2025 | 76 | F | Breast | 7.5 × 7 × 6 | No | Retained | Mastectomy | Alive |
| NA | *1 doxorubicin+ifosfamide+mesna | ||||||||
| *2 vincristine+cyclophosphamide+doxorubicin/ifosfamide+etoposide |
NA, not available.