Figure 2.

Caroli’s disease. MRI cholangiography with maximum intensity projection (A) showing multifocal cystic dilatations of the intrahepatic bile ducts (arrow). Contrast-enhanced T1-weighted sequence (B) showing the central dot sign, representing a portal branch in the middle of the dilated bile duct (arrow), which is quite characteristic of this condition. C: Contrast-enhanced CT scan of a patient with Caroli’s disease, in the pyelographic phase, showing dilatation of the biliary tree (arrow) and medullary sponge kidneys (asterisks).