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. Author manuscript; available in PMC: 2025 May 19.
Published in final edited form as: Expert Rev Hematol. 2022 Feb 28;15(4):359–368. doi: 10.1080/17474086.2022.2043743

Table 1:

Risk of bias in the included studies

Reference Q1 Q2 Q3 Q4 Q5 Q6 Q7 Q8 Q9 Risk of bias score Risk of bias
Genetic data
Bhatnagar No Yes Yes Yes Yes Yes No Yes Yes 7 Moderate
Descriptive / Cross-sectional studies
Campbell No Yes Yes Yes Yes NA No Yes Yes 6 Moderate
Desai No No No Yes Yes NA No Yes Yes 4 High
Johnson No Yes Yes Yes Yes NA No Yes Yes 6 Moderate
Strumph No Yes Yes Yes Yes NA No Yes Yes 6 Moderate
Lamarre No Yes Yes Yes Yes NA No Yes Yes 6 Moderate
Lemonne No Yes Yes Yes Yes NA No Yes Yes 6 Moderate
Oguanobi No No Yes Yes Yes NA No Yes Yes 5 High
Pegelow No Yes Yes Yes Yes NA No Yes Yes 6 Moderate
Pikilidou No Yes Yes Yes Yes NA No Yes Yes 6 Moderate
Cohort / Case control studies
Gordeuk Yes Yes Yes No Yes Yes No Yes Yes 7 Moderate
Grell No Yes Yes Unclear Yes Yes Unclear Yes Yes 6 Moderate
Homi No Yes Yes Yes Yes Yes Unclear Yes Yes 7 Moderate
Kuma Yes Yes Yes Yes Yes Yes Unclear Yes Yes 8 Low
Makubi No Yes Yes Yes Yes Yes Unclear Yes Yes 7 Moderate
Novelli Yes Yes Yes Yes Yes Yes Unclear Yes Yes 8 Low