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. Author manuscript; available in PMC: 2025 May 19.
Published in final edited form as: Expert Rev Hematol. 2022 Feb 28;15(4):359–368. doi: 10.1080/17474086.2022.2043743

Table 2:

Characteristics of included studies

Studies Year Countries Study settings Sample size Methodology Charateristics of study participants Outcomes Identified factors
Bhatnagar [26] 2013 United States (USA) SCD cohorts of African American ancestry 1,617 patients Genome-wide meta-analysis This study includes two African American ancestry SCD cohorts. Gender: 843 males, 774 females. Average age was 8.96 from one cohort and 9.57 years from the second cohort Systolic blood pressure (SBP) Genetic factors
Campbell [35] 2007 Jamaica SCD clinic 51 subjects with HbSC and 88 subjects with HbSS Cross-sectional 51 subjects with HbSC (29 males, 22 females) and 88 subjects with HbSS (43 males, 45 females) Age: Age ranged from 23.1 to 31.6 years. Blood pressure (BP) and BP by genotype Anthropometric, haematological and renal functional factors
Desai [15] 2012 USA SCD patients cohort at University of North Carolina (UNC) clinic 156 SCD patients in the UNC cohort Cross-sectional Age: Mean age was 36 years (range 27–47) Gender: 97 (62%) females Ethinicity: 154 (99%) african american SBP and diastolic blood pressure (DBP) Clinical and laboratory factors
Gordeuk [10] 2008 USA Patients from Sickle Cell Pulmonary Hypertension Screening Study 163 SCD patients Retrospective cohort cohort Adults with hemoglobin SS or Sβ0 thalassemia patients Relative systemic hypertension (RSH) (i.e., SBP 120–139 mm Hg or DBP 70–89 mm Hg) Complications associated
Grell [13] 1981 Jamaica SCD clinic of the University Hospital in Jamaica. 70 SCD patients Retrospective cohort Participants were aged over 30 years. Gender: 29 males and 41 females. Age: age ranged from 30 to 69 years. SBP and DBP Age and gender
Homi [21] 1993 Jamaica SCD clinic of the University Hospital of the West Indies, Kingston, Jamaica. 342 SCD patients Retrospective cohort Adults aged 9.5 to 18.5 years.220 with homozygous SS and 122 with hemoglobin C BP Weight
Johnson [18] 1981 USA SCD clinics at the Los Angeles County-University of Southern California Medical Center and The Martin Luther King, Jnr General Hospital. 187 SCD patients Cross-sectional Gender: 81 males, 106 females Age: mean age was 29 years (range 18–67). 130 sickle cell anemia, 43 sickle cell-hemoglobin C, 15 had sickle cell thalassemia Prevalence and severity of hypertension in SCD Haemoglobinopathy, age and advancing age
Strumph [14] 2021 USA Children’s hospital 100 patients with SCD Cross-sectional 100 SCD patients with age ranging from 5 to 21 Nocturnal hypertension Complication associated
Kuma [16] 2018 Ghana The Ghana Institute of Clinical Genetics 875 with homozygous or compound heterozygous SCD Retrospective cohort Participants were adults aged >18 years. Gender: 63 % were females. Age: Median age was 31 ( range 23–44) Prevalence of RSH Complications associated
Lamarre [20] 2013 (Guadeloupe, French West Indies) SCD Center at the Academic Hospital of Pointe-à-Pitre. 97 SCD patients Cross-sectional Adults aged ≥18 years. Gender: 43 male and 54 females RSH and systematic hypertension Biological factors
Lemonne [24] 2014 (Guadeloupe, French West Indies). SCD Center at the Academic Hospital of Pointe-à-Pitre. 89 SCD patients (sickle cell-hemoglobin C) Cross-sectional Gender: 40 males, 49 females Age: mean age was 38 ± 13 years RSH Blood Viscosity
Makubi [17] 2017 Tanzania Patient were identified at paediatric or haematology clinics or during hospitalization 1013 SCD patients Retrospective cohort Gender: 56% were females Age: Median age was 17 (range15–22) RSH and systematic hypertension Any risk factors
Novelli [25] 2014 USA Multicentre international sickle cell trial (USA and United Kingdom) 661 SCD patients Retrospective cohort Participants were adults: 500 HbSS and 161 HbSC, with mean age 34 (range 25–45) and 41 (range 28 –51) Pulse pressure Markers of haemolysis
Oguanobi [19] 2010 Nigeria Outpatient sickle cell clinics and the cardiac center of the University of Nigeria Teaching Hospital, Enugu, Nigeria 62 SCD patients Cross-sectional Participants were adults. Age: Mean age was 28.27(range 18–44) Arterial BP Age, gender, and anthropometric data
Pegelow [23] 1997 USA Cooperative Study of Sickle Cell Disease (CSSCD) at at 23 clinical centers, USA 3,317 SCD patients Cross-sectional Participants included were children and adults (2 years old or older) BP Age, gender, anthropometric, clinical and laboratory data
Pikilidou [22] 2015 Greece SCD center 45 SCD patients Cross-sectional Participants were adults. Age: Mean age was 43 years (range 26–65) Body mass index (BMI):(24.1 ± 3.6 kg/m2 Gender: 30 males and 15 females BP Arterial stiffness