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. 2025 May 20;14:RP104979. doi: 10.7554/eLife.104979

Key resources table.

Reagent type (species) or resource Designation Source or reference Identifiers Additional information
Genetic reagent, KI-mouse (Mus musculus male and female) Q175 KI CHDI-81003003 N/A Knock-in Mouse
human HTT exon 1 sequence containing a ~190 CAG repeat tract
Genetic reagent,
Transgenic (Mus musculus male and female)
TRGL6 Lee et al., 2019 N/A Transgenic with Thy1 promoter
Genetic reagent,
Transgenic (Mus musculus male and female)
cross with KI (Mus musculus male and female)
Q175/TRGL This study N/A Crossed the zQ175 KI with the TRGL6 mice
Sequence-based reagent Forward primer for genotyping TRGL:
50-CTT TCC CCA CAG AAT CCA AGT CGG AAC-30
Lee et al., 2019
Sequence-based reagent Reverse primer for genotyping TRGL:
50-GCA CGA ATT CGG GCG CCG GTG GAG TGG CGG-30
Lee et al., 2019
Antibody tHTT Cell Signaling Technology Cat# 5656; RRID:AB_10827977 WB: 1:1000
Antibody ntHTT mEM48 Millipore sigma Cat# MAB5374; RRID:AB_177645 WB 1:200
IHC 1:50
Antibody HTT 1C2 Millipore sigma Cat# mab1574; RRID:AB_94263 WB 1:1000
Antibody HTT human Millipore sigma Cat# mab5490; RRID:AB_2233522 WB 1:1000
IHC 1:200
Antibody HTT MW8 Develop Studies Hybridoma Bank, University of Iowa Cat# MW8; RRID:AB_528297
Antibody HTT PHP2 CHDI/Coriell Cat# CHDI-90001516–2
Antibody MTOR Cell Signaling Technology Cat# 2983; RRID:AB_2105622 WB: 1:1000
Antibody p-MTOR S2481 Cell Signaling Technology Cat# 2874 WB 1:1000
Antibody p-MTOR S2448 Cell Signaling Technology Cat# 2971; RRID:AB_330970 WB: 1:1000
Antibody p70S6K Cell Signaling Technology Cat# 2708; RRID:AB_390722 WB: 1:1000
Antibody p-p70S6K S371 Cell Signaling Technology Cat#: 9208 WB: 1:1000
Antibody p-p70S6K T389 Cell Signaling Technology Cat# 9234; RRID:AB_2269803 WB: 1:1000
Antibody S6 ribosomal Cell Signaling Technology Cat# 2317; RRID:AB_2238583 WB: 1:1000
Antibody p-S6 ribosomal S240/S244 Cell Signaling Technology Cat# 5364; RRID:AB_10694233 WB: 1:1000
Antibody ULK1 Cell Signaling Technology Cat# 6439; RRID:AB_11178933 WB: 1:500
Antibody p-ULK S757 Cell Signaling Technology Cat# 6888; RRID:AB_10829226 WB: 1:500
Antibody p-ULK S317 Cell Signaling Technology Cat# 37762; RRID:AB_2922992 WB: 1:500
Antibody ATG5 Cell Signaling Technology Cat# 12994; RRID:AB_2630393 WB: 1:1000
Antibody ATG5 Millipore sigma Cat# abc14 WB: 1:750
IHC 1:500
Antibody ATG14 Cell Signaling Technology Cat# 5504; RRID:AB_10695397 WB: 1:1000
Antibody p-ATG14 S29 Cell Signaling Technology Cat# 92340; RRID:AB_2800182 WB: 1:1000
Antibody Beclin 1 BD Bioscience Cat# 612113; RRID:AB_399484 WB: 1:1000
Antibody p-Beclin 1 S30 Cell Signaling Technology Cat# 35955 WB: 1:1000
Antibody VPS34 Cell Signaling Technology Cat# 4263 WB 1:1000
Antibody p-VPS34 S249 Cell Signaling Technology Cat# 13857; RRID:AB_2798332 WB 1:1000
Antibody TRAF6 Cell Signaling Technology Cat# 8028 WB 1:1000
Antibody LC3 Millipore sigma Cat# abc929 WB 1:500
IHC 1:100
Antibody LC3 Novus Biologics Cat# NB100-2220; RRID:AB_10003146 WB 1:1000
IHC 1:200
Antibody p62/sqstm1 BD Biosciences Cat# 610832; RRID:AB_398152 WB 1:2000
IHC 1:200
Antibody p62/SQSTM1 c-term Progen Biotechnik Cat# GP62-C; RRID:AB_2687531 WB 1:1000
IHC 1:250
Antibody Ubiquitin Dako Agilent Cat# z0458; RRID:AB_2315524
Antibody Ubiquitin Abcam Cat# ab7780; RRID:AB_306069
Antibody LAMP1 Develop Studies Hybridoma Bank, University of Iowa Cat# H4A3; RRID:AB_2296838 IHC 1:50
Antibody CTSB Neuromics Cat# GT15047; RRID:AB_2737184 WB 1:5000
IHC 1:500
Antibody CTSD In house RU4 WB 1:10,000
IHC 1:5000
Antibody CTSD sheep In house D-2–3 WB 1:1000
IHC 1:500
Antibody DARPP32 Abcam Cat# ab40801; RRID:AB_731843 WB 1:1000
IHC 1:100
Antibody NeuN Millipore Sigma Cat# mab377; RRID:AB_2298772 IHC 1:400
Antibody β−actin Millipore Sigma Cat# A1978; RRID:AB_476692 WB 1:10,000
Antibody Goat anti-rabbit secondary Vector Laboratories Cat# 68–4140 IHC: 1:500
Antibody Goat anti-mouse secondary Vector Laboratories Cat# BA-9200 IHC: 1:500
Antibody Alexa Fluor 488-conjugated goat anti-rabbit IgG Thermo Fisher Scientific Cat# A11034; RRID:AB_2576217 IHC: 1:500
Antibody Alexa Fluor 568- goat anti-rabbit IgG Thermo Fisher Scientific Cat# A11036; RRID:AB_10563566 IHC: 1:500
Antibody Alexa Fluor 647- goat anti-rabbit IgG Thermo Fisher Scientific Cat# A21245; RRID:AB_2535813 IHC: 1:500
Antibody Alexa Fluor 405- goat anti-rabbit IgG Thermo Fisher Scientific Cat# A48254; RRID:AB_2890548 IHC: 1:500
Antibody Alexa Fluor 568- goat anti-mouse IgG Thermo Fisher Scientific Cat# A11031; RRID:AB_144696 IHC: 1:500
Antibody Alexa Fluor 647- goat anti-mouse IgG Thermo Fisher Scientific Cat# A21235; RRID:AB_2535804 IHC: 1:500
Antibody Alexa Fluor 568- goat anti-rat IgG Thermo Fisher Scientific Cat# A21247; RRID:AB_141778 IHC: 1:500
Antibody Donkey anti-Rabbit IgG HRP Jackson ImmunoResearch Cat# 711-035-152; RRID:AB_10015282 WB: 1:5000
Antibody Donkey anti-Mouse IgG HRP Jackson ImmunoResearch Cat# 712-035-150; RRID:AB_2340638 WB: 1:5000
Antibody Donkey anti-goat IgG HRP Jackson ImmunoResearch Cat# 705-035-003; RRID:AB_2340390 WB: 1:5000
Antibody 10 nm gold anti mouse IgG Electron Microscopy Sciences Cat# 25129 IEM 1:50
Antibody 10 nm gold anti rabbit IgG Electron Microscopy Sciences Cat# 25109 IEM 1:50
Chemical compound, drug INK (mTOR i) ChemScene CAS 1224844-38-5 Dissolved in 0.5% carboxymethyl cellulose (Sigma, Cat #5678) and 0.05% tween 80 in water
Chemical compound, drug PBS Thermo Fisher Scientific Cat# BP339-4
Chemical compound, drug Sodium cacodylate buffer Electron Microscopy Sciences Cat#11652 0.1 M for fixation of brains
Chemical compound, drug Paraformaldehyde Electron Microscopy Sciences Cat#15714 4% for fixation of brains
Chemical compound, drug 25% glutaraldehyde Electron Microscopy Sciences Cat# 16220
Chemical compound, drug Uranyl acetate Electron Microscopy Sciences Cat# 22400–4 EM processing
Chemical compound, drug Lead citrate Electron Microscopy Sciences Cat#22410 EM processing
Chemical compound, drug Osmium tetroxide Ted Pella Cat#18465 EM processing
Chemical compound, drug Sodium metaperiodate Sigma-Aldrich Cat#S1878-25g EM processing
Chemical compound, drug Permount Electron Microscopy Sciences Cat# 17986 Dab IHC
Chemical compound, drug Flouro-gel Electron Microscopy Sciences Cat# 17985–10 IF IHC
Chemical compound, drug FBS Thermo Fisher Scientific Cat# 26140 IHC blocking
Chemical compound, drug Horse serum Thermo Fisher Scientific Cat# 16050 IHC blocking
Chemical compound, drug Spurr resin Electron Microscopy Sciences Cat# 14300
Commercial assay kit Vectastain ABC Vector Laboratories Cat# PK-4000; RRID:AB_2336818 For DAB staining
Commercial assay kit DAB Peroxidase Substrate kit Vector Laboratories Cat# SK-4100; RRID:AB_2336382 For DAB staining
Commercial assay kit HQ silver kit NanoProbes Cat# 2012–45 ml EM processing
Software ImageJ NIH https://imagej.nih.gov/ij/
Software Excel Microsoft Microsoft 365
Software GraphPad Prism 8.0.1 GraphPad
Other Nitrocellulose membrane Whatman WB 0.2µm-pore
Other Aclar embedding film Electron Microscopy Sciences Cat# 50425–25 EM processing
Other 75 mesh nickel grids with carbon coating and formvar Electron Microscopy Sciences Cat# pi-75-ni-25 EM processing
Other EM block Electron Microscopy Sciences Cat# 25596 EM processing