| PH | pulmonary hypertension |
| ILD | interstitial lung disease |
| PH-ILD | pulmonary hypertension associated interstitial lung disease |
| PVR | pulmonary vascular resistance |
| WU | Wood units |
| CPET | cardiopulmonary exercise testing |
| mPAP | mean pulmonary arterial pressure |
| eRVSP | estimated right ventricular systolic pressure |
| PCWP | pulmonary capillary wedge pressure |
| RV | right ventricular |
| 6MWD | six-minute walk distance |
| RHC | right heart catheterization |
| WHO | World Health Organization |
| FC | functional class |
| WHO-FC | World Health Organization Functional Class |
| CT | computed tomography |
| PVRS | non-significant change in pulmonary vascular resistance during exercise |
| PVRD | increase in pulmonary vascular resistance during exercise |
| PFTs | Pulmonary function tests |
| FVC | forced vital capacity |
| DLCO | diffusing capacity for carbon monoxide |
| UIP | usual interstitial pneumonia |
| NSIP | nonspecific interstitial pneumonia |
| CPFE | combined pulmonary fibrosis and emphysema |
| PDE5 | Phosphodiesterase-5 |