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. 2025 Aug 5;16:1592655. doi: 10.3389/fendo.2025.1592655

Table 3.

Syndromic conditions associated to congenital hypothyroidism and correlated genes.

Type of CH Syndrome Gene
Thyroid Dysgenesis Brain-Lung-Thyroid syndrome Nkx2.1 (Ttf-1)
Di George syndrome TBX1
Bamforth-Lazaryus syndrome FOXE1
Williams-Beuren syndrome ELN, BAZ1B
Kabuki syndrome KMT2D, KDM6A
Down syndrome DYRK1A
Townes-Brocks syndrome SALL1
Johanson-Blizzard syndrome URB1
Ohdo syndrome KAT6B
Takenouchi-Kosaki syndrome CDC42
Blepharo-cheilo-dontic syndrome CDH1, CTNND1
Dyshormonogenesis Pendred syndrome SLC26A4/PDS
Pseudohypoparathyroidism GNAS