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. 2025 Sep 1;18:12021–12044. doi: 10.2147/JIR.S534574

Table 1.

Summary of Animal Models of Mitochondrial ROS and Rheumatic Diseases Pathogenesis

Genes/Interventions Animal Model Phenotype/Effects References
TNF-α overexpression HLA-B27 transgenic rat Spontaneous inflammatory arthritis, colitis Taurog et al90
IL-23/IL-17 axis inhibition Mouse CIA Reduced synovitis and bone erosion Sherlock et al91
MRL/lpr mouse model MRL/lpr mouse SLE: autoantibodies, glomerulonephritis Theofilopoulos et al92
BAFF blockade NZB/W F1 mouse (SLE) Delayed autoantibody production, improved survival Stohl et al93
HLA-DR4 transgenic DR4-Tg mouse Autoimmune arthritis with citrullinated peptide reactivity Lundberg et al94
Anti-dsDNA antibody induction BALB/c mouse (SLE) Glomerular immune complex deposition Kaliyaperumal et al95
NOD mouse model NOD mouse Sjögren’s syndrome: salivary gland inflammation Gao et al96
STAT4 knockout Mouse CIA Reduced Th1/Th17 differentiation, milder arthritis Thieu et al97
IL-6 receptor antagonist Rat adjuvant-induced arthritis (AIA) Suppressed synovial hyperplasia Mihara et al98
TGF-β1 overexpression Transgenic mouse Fibrosis in scleroderma-like skin disease Krzistetzko et al99
CD4+ T cell depletion Mouse K/BxN serum transfer Attenuated joint inflammation Kouskoff et al100
Rituximab (anti-CD20) Pristane-induced lupus mouse Reduced autoantibodies and kidney damage Satoh et al101
ANKH gene mutation Progressive ankylosis mouse (ank/ank) Spontaneous joint calcification (ankylosis) Ho et al102