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. 2025 Sep 12;104(37):e44309. doi: 10.1097/MD.0000000000044309

Table 7.

Incidence of PKU by populations.[2,3,4143]

Continents Countries Incidence of PKU
Asian populations China 1 in 17,000
Korea 1 in 41,000
Japan 1 in 125,000
India 1 in 6000
Turkey 1 in 4200
European populations Ireland 1 in 4500
Scotland 1 in 5300
Czechoslovakia 1 in 7000
Hungary 1 in 11,000
Denmark 1 in 12,000
France 1 in 13,500
Norway 1 in 14,500
United Kingdom 1 in 14,300
Italy 1 in 17,000
Finland 1 in 200,000
North America United States (Caucasians) 1 in 10,000
Canada 1 in 22,000
Oceania Australia 1 in 10,000
Latin American countries Brazil 1 in 25,294
Argentina 1 in 27,275
Chile 1 in 19,510

PKU = phenylketonuria.