SCA1	Spinocerebellar ataxia type 1
CAG	cytosine–adenine–guanine
ATXN1	ataxin-1
Ser776	serine 776
ASO	antisense oligonucleotide
RNAi	RNA interference
NfL	neurofilament light protein
iPSC	induced pluripotent stem cell
NLS	nuclear localization signal
UPS	ubiquitin–proteasome system
ATXN1-CIC	ataxin-1-Capicua
CIC	Capicua
HMGB ½	High-Mobility Group Box ½
LANP	leucine-rich acidic nuclear protein
PKA	protein kinase
RBM17	RNA-Binding Motif Protein 17
U2AF65	U2 snRNP auxiliary factor 65 kDa
NLK	Nemo-like kinase
ISG15	Interferon-stimulated gene 15
GFI1	growth factor independence 1
SMRT	Silencing Mediator of Retinoid and Thyroid Receptors
Tip60	Tat-interacting protein 60
RORα	retinoid-related orphan receptor α
Boat1	ATXN1-like paralog
RPA	replication protein A
ASR	acoustic startle response
FST	forced swim test
CaB	calbindin
PV	Parvalbumin
CCK	cholecystokinin
LPS	lipopolysaccharide
Ara-C	Cytarabine