Table 1.
Characteristic | No. ofFamilies | Average Age(years)at Diagnosisof GenotypedAffectedIndividuals (SD) | Average No.of AffectedMen perFamily (Range) | Average No.of AffectedMen Genotypedper Family(Range) |
All families | 172 | 62.7 (9.43) | 3.8 (2–14) | 2.6 (2–7) |
White | 154 | 63.1 (9.31) | 3.7 (2–13) | 2.6 (2–7) |
Black | 16 | 59.7 (9.64) | 5.1 (2–14) | 2.5 (2–4) |
Asian/Pacific Islander | 2 | 56.4 (12.82) | 5.0 (5) | 2.0 (2) |
<5 affected members | 148 | 62.7 (9.60) | 3.3 (2–4) | 2.4 (2–4) |
⩾5 affected members | 24 | 62.4 (8.63) | 7.1 (5–14) | 3.3 (2–7) |
Average age at diagnosis <66 years | 108 | 59.8 (8.98) | 3.7 (2–14) | 2.5 (2–5) |
Average age at diagnosis ⩾66 years | 64 | 67.4 (8.14) | 4.1 (3–12) | 2.6 (2–7) |
Male-to-male transmission | 122 | 62.7 (9.86) | 4.1 (2–14) | 2.6 (2–7) |
No male-to-male transmission | 50 | 62.5 (8.26) | 3.1 (2–6) | 2.5 (2–5) |