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. 2025 Dec 11;41(3):903–905. doi: 10.1007/s00467-025-07087-4

Table 1.

Summary of Ongoing and recently Completed Clinical Trials for AS This table provides an overview of interventional studies currently evaluating or recently completing evaluation of investigational therapies in AS, including mechanism of action, target population, and study status

Study name Drug Mechanism Population Status Sponsor
EPPIK Sparsentan Dual ETA/AT1 receptor blocker Pediatrics & Adolescents

Recruiting

(Phase 2)

Travere Therapeutics
ALPESTRIA-1 Vonafexor FXR agonist Adolescents & Adults

Active, not recruiting

(Phase 2)

ENYO Pharma
ELX-02 ELX-02 Read-through compound (COL4 mutations) Pediatrics & Adults

Ongoing

(Phase 2)

Eloxx Pharmaceuticals
FIONA Finerenone Non-steroidal MRA Pediatrics & Adults

Recruiting

(Phase 3)

Bayer
R3R01-201 R3R01 Mediates cholesterol efflux by ABCA1 induction Adolescents & Adults

Completed

(Phase 2)

River 3 Renal Corporation
VAR200-0301 2HPβCD Mediates cholesterol efflux Adults

Ongoing

(Phase 2)

ZyVersa
hUC-MSC hUC-MSC

Stem cell therapy

(anti-inflammation)

Pediatrics

Planned

(Phase 2)

Guangzhou Women& Children’s

Medical Center

Setanaxib Setanaxib

NOX1/4 inhibitor

(anti-fibrotic)

Adolescents & Adults

Completed

(Phase 2)

Calliditas Therapeutics
AFFINITY Atrasentn Selective ETA receptor antagonist Adults

Active, not recruiting

(Phase 2)

Novartis Pharmaceuticals
CARDINAL Bardoxolone methyl Nrf2 activator Adolescents & Adults

Completed, negative

(Phase 3)

Biogen
EAGLE Bardoxolone methyl Nrf2 activator (long-term safety) Adolescents & Adults

Terminated

(Phase 3)

Biogen
HERA Lademirsen (anti-miR-21) microRNA inhibitor Adolescents & Adults Terminated for futility Sanofi
DOUBLE PRO-TECT Alport Dapagliflozin SGLT2 inhibitor Adolescents & Young Adults Recruiting (Phase 3) German Research Foundation DFG