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. 2026 Feb 6;18(2):216. doi: 10.3390/v18020216
PrP Prion protein
PrPC Cellular prion protein (normal form)
PrPSc Scrapie-associated pathological prion protein
TSE Transmissible spongiform encephalopathy
CJD Creutzfeldt–Jakob disease
sCJD Sporadic Creutzfeldt–Jakob disease
gCJD/fCJD Genetic/familial Creutzfeldt–Jakob disease
vCJD Variant Creutzfeldt–Jakob disease
iCJD Iatrogenic Creutzfeldt–Jakob disease
FFI Fatal Familial Insomnia
GSS Gerstmann-Sträussler-Scheinker disease
RPD Rapidly progressive dementia
PRNP Prion protein gene
129M/V Methionine/Valine polymorphism at codon 129 of PRNP
MM, MV, VV Methionine/Methionine; Methionine/Valine; Valine/Valine genotypes
Type 1/Type 2 PrPSc Electrophoretic prion protein types
E200K, D178N, P102L, V180I, etc. Common PRNP pathogenic mutations
PSWCs Periodic Sharp Wave Complexes (EEG hallmark)
MRI Magnetic resonance imaging
DWI Diffusion-weighted imaging
ADC Apparent diffusion coefficient
FLAIR Fluid-attenuated inversion recovery
CT Computed tomography
PET Positron emission tomography
FDG-PET Fluorodeoxyglucose positron emission tomography
CSF Cerebrospinal fluid
RT-QuIC Real-Time Quaking-Induced Conversion
qRT-QuIC/2G-RT-QuIC First or second generation RT-QuIC
t-tau Total tau protein
p-tau Phosphorylated tau
NfL Neurofilament light chain
14-3-3 CSF 14-3-3 protein
EEG Electroencephalography