Table V.
Elevated levels of Tricarboxylic acid (TCA) cycle intermediates and acylcarnitines.
| Analyte Detected at Increased Level in the Patient’s Blood Sample | Z-score | Human Metabolome Database (HMDB) Code |
|---|---|---|
| Alpha-ketoglutarate | 2.9 | HMDB0000208 |
| Aconitate [cis or trans] | 2.2 | HMDB0000958 |
| Fumarate | 2.1 | HMDB0000134 |
| Myristoleoylcarnitine (C14:1)’ | 2.6 | HMDB0240588 |
| Laurylcarnitine (C12) | 2.5 | HMDB000225 |
| 3-hydroxysebacate | 2.5 | HMDB0000350 |
| Hexanoylcarnitine (C6) | 2.4 | HMDB0000756 |
| Oleoylcarnitine (C18:1) | 2.2 | HMDB0005065 |