| AAO-HNS | American Academy of Otolaryngology–Head and Neck Surgery |
| AD | Autosomal dominant |
| AIED | Autoimmune inner ear disease |
| ATP1A2 | ATPase Na+/K+ Transporting Subunit Alpha 2 |
| ATP6V0E | ATPase H+ Transporting V0 Subunit E1 |
| CACNA1A | Calcium Voltage-Gated Channel Subunit Alpha1 A |
| DRD1 | Dopamine Receptor D1 |
| EAONO | European Academy of Otology and Neurotology |
| EH | Endolymphatic hydrops |
| FMD | Familial Ménière’s disease |
| FHM | Familial hemiplegic migraine |
| GABRP | Gamma-Aminobutyric Acid Type A Receptor Subunit Pi |
| HCFC1 | Host Cell Factor C1 |
| HLA | Human leukocyte antigen |
| HRH2 | Histamine Receptor H2 |
| IL-1β | Interleukin-1 beta |
| IL-6 | Interleukin-6 |
| KCNMB1 | Potassium Calcium-Activated Channel Subfamily M Regulatory Beta Subunit 1 |
| KCNIP1 | Potassium Voltage-Gated Channel Interacting Protein 1 |
| LYP | Lymphoid tyrosine phosphatase |
| MD | Ménière’s disease |
| MICA | MHC class I chain-related gene A |
| MSG | Mmonosodium glutamate |
| NFKB1 | Nuclear Factor Kappa B Subunit 1 |
| OSA | Obstructive sleep apnea |
| PTPN22 | Protein Tyrosine Phosphatase Non-Receptor Type 22 |
| SCN1A | Sodium Voltage-Gated Channel Alpha Subunit 1 |
| SLC34A1 | Solute Carrier Family 34 Member 1 |
| SMD | Sporadic Ménière’s disease |
| T3 | Triiodothyronine |
| T4 | Thyroxine |
| TLR10 | Toll-like receptor 10 |
| TNF-α | Tumor necrosis factor |