TABLE 3.

Urine amino acids (n = 3)

Amino acid	Concn (μM) in mice with genotype
	+/+	MAAI	MAAI/FAH
Phe	69	45	123
Tyr	103	232	3,377
Met	59	75	402
Ala	268	228	1,387
Gly	457	446	1,531
Leu	282	285	1,263
Arg	88	166	312
Gln	0	320	4,963
Orn	53	33	260
Glu	284	72	0
Tau	511	715	1,723
Pho	1,345	1,134	1,970
Arg	88	170	312
His	56	59	824
Lys	148	136	797
Asp	207	172	1,075
Thr	0	237	2,037
GlcNH2a	199	345	747

^aGlcNH₂, glucosamine.