Skip to main content
. 2026 Jul 18;27(14):6404. doi: 10.3390/ijms27146404
ACG American College of Gastroenterology
AGA American Gastroenterological Association
AISP Italian Association for the Study of the Pancreas
ASCO American Society of Clinical Oncology
AT Ataxia–Telangiectasia
BD-IPMN Branch-Duct IPMN
BER Base Excision Repair
CAPS International Cancer of the Pancreas Screening
CDKN2A Cyclin-Dependent Kinase Inhibitor 2A
CFTR Cystic Fibrosis Transmembrane Conductance Regulator
CI Confidence Interval
CR Complete Response
CT Computed tomography
DDR DNA Damage Repair
dMMR Mismatch Repair Protein Deficiency
DPCA Dutch Pancreatic Cancer Audit
DSB Double-Strand Break
EUROPAC European Registry of Hereditary Pancreatitis and Pancreatic Cancer
EUS Endoscopic Ultrasonography
FAMM Familial Atypical Multiple Mole Melanoma
FAP Familial Adenomatous Polyposis
FNA Fine-Needle Aspiration
FNB Fine-Needle Biopsy
FPC Familial Pancreatic Cancer
GenoMEL Melanoma Genetics Consortium
HBOC Hereditary Breast and Ovarian Cancer
HP Hereditary Pancreatitis
HPC Hereditary Pancreatic Cancer
HR Homologous Recombination
HRD Homologous Recombination Deficiency
HRHR Homologous Recombination
HRI High-Risk Individual
ICI Immune Checkpoint Inhibitor
IPMN Intraductal Papillary Mucinous Neoplasm
IRFARPC Italian Registry of Families At Risk of Pancreatic Cancer
LAPCR Locally Advanced Pancreatic Cancer Registry
LFS Li–Fraumeni Syndrome
LS Lynch Syndrome
MD-IPMN Main Duct-IPMN
MLH1 MutL Homolog 1
MMR Mismatch Repair
MRCP Magnetic Resonance Cholangiopancreatography
MRI Magnetic Resonance Imaging
MSH2 MutS Homolog 2
MSH6 MutS Homolog 6
MSI Microsatellite Instability
MSI-H MSI-High
MSI-I MSI-Indeterminate
MSS Microsatellite Stable
NCCN National Comprehensive Cancer Network
NCR Netherlands Cancer Registry
OGV Pathogenic Germline Variant
ORR Objective Response Rate
OS Overall Survival
PANGENFAM Spanish Familial Pancreatic Cancer Registry
PanIN Pancreatic Intraepithelial Neoplasia
PARPi Poly-(ADP-ribose) Polymerase inhibitor
PC Pancreatic Cancer
PFS Progression-Free Survival
PGPV Presumed Germline Pathogenic Variant
PGV Pathogenic Germline Variants
PJS Peutz–Jeghers Syndrome
PMS-2 Post-Meiotic Segregation increased 2
PRECEDE Pancreatic Cancer Early Detection Consortium
PRSS1 Protease Serine 1
RER+ Replication Error—positive
RR Relative Risk
SEER Surveillance, Epidemiology, and End Results
SPINK1 Serine Protease Inhibitor Kazal type 1
SSB Single-Strand Breaks
STK11 Serine/Threonine Kinase 11
TMN Tumor Mutational Burden