| ANKH | Inorganic Pyrophosphate Transport Regulator |
| BCAA | Branched-chain amino acid |
| bSEM | Backscattered scanning electron microscopy |
| CIC | Mitochondrial citrate carrier |
| DEE25 | Developmental and epileptic encephalopathy 25 with amelogenesis imperfecta |
| EDTA | Disodium ethylenediaminetetraacetic acid |
| EOE | Enamel organ epithelium |
| FIB-SEM | Focused ion beam–scanning electron microscopy |
| GC-MS | Gas Chromatography–Mass Spectrometry |
| LAMP1 | Lysosomal-Associated Membrane Protein 1 |
| MAT | Enamel/dentin matrix |
| MES | Pulpal mesenchyme |
| MIM | Mendelian Inheritance in Man |
| MMRRC | Mutant Mouse Resource and Research Centers |
| NaCT | Sodium-dependent citrate transporter |
| PCR | Polymerase chain reaction |
| PFA | Paraformaldehyde |
| RPM | Revolutions per minute |
| Slc4a4 | Solute Carrier Family 4 Member 4 |
| Slc13a2 | Solute Carrier Family 13 Member 2 |
| Slc13a3 | Solute Carrier Family 13 Member 3 |
| Slc13a5 | Solute Carrier Family 13 Member 5 |
| Slc25a1 | Solute Carrier Family 25 Member 1 |
| TCA | Tricarboxylic acid |
| WT | Wild-type |