Table 1. Clinicopathological features of previously reported cases of MELTVR and the present case.
ER: estrogen receptor, PgR: progesterone receptor, EMA: epithelial membrane antigen, α-SMA: α smooth muscle actin, CK: Cytokeratin , AR: androgen receptor, +: positive, -: negative, NR: not reported
| Author | Age | Clinical presentation | Tumor size | Histological findings | Immunohistochemistry | SMARCB1 | Treatment | Margin | Outcome | |
| Yoshida et al. [1] | 24–70 | Vulvar mass/nodule | Variable | Spindle to epithelioid cells with myxoid and hypercellular areas | ER + PgR + EMA + | variable α-SMA | Lost | Surgical excision | Variable | Mostly favorable (1-172 months) |
| Liu et al. [2] | 43 | Vulvar mass | 3.5 cm | Myxoid and solid components with spindle/plasmacytoid cells | Lost | Wide local excision | NR | No recurrence | ||
| Urakami et al. [3] | 54 | Vulvar tumor after inguinal tumor excision | 4 cm | Lobulated tumor with myxoid stroma | ER + PgR + | Lost | Surgical excision | Negative | No recurrence (10 months) | |
| Aminimoghaddam et al. [4] | 46 | Subcutaneous vulvar nodules with recent enlargement and discomfort; mass involving the right labia majora and mons pubis | 10 cm | Myxoid mesenchymal tissues. A mild to moderate atypia. No mitosis or necrosis | Vimentin + | Lost | Surgical resection | NR | Recurrence (36 months) | |
| Kamboj et al. [5] | 47 | A mobile swelling in the subcutaneous region of right labia majora | 3 cm | Solid sheets of cells with a predominant epithelioid to rhabdoid morphology and focal areas of spindling | ER + EMA + | CK - | Lost | Surgical resection | NR | No recurrence (6 months) |
| Present case | 23 | Myxoid and hypercellular areas with spindle to plasmacytoid cells, necrosis, and mitotic activity | 4.5 cm | Myxoid and hypercellular areas with spindle to plasmacytoid cells, necrosis, and mitotic activity | ER + PgR + EMA + | AR + | Lost | Surgical excision | Negative | No recurrence (3 months) |