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. 1995 Jul;37(1):144–147. doi: 10.1136/gut.37.1.144

Chronic intrahepatic cholestasis in sickle cell disease requiring exchange transfusion.

A O'Callaghan 1, S G O'Brien 1, M Ninkovic 1, G P Butcher 1, C S Foster 1, J R Walters 1, I A Roberts 1
PMCID: PMC1382787  PMID: 7672666

Abstract

A 15 year old boy with sickle cell disease developed intrahepatic cholestasis. A course of exchange transfusion successfully corrected the extreme hyperbilirubinaemia over one year. Upon stopping the exchange transfusion programme the hyperbilirubinaemia relapsed but transfusion was effective when reinstituted.

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Selected References

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