Table 1.

Porphobilinogen deaminase (PBGD) activities in tissues from PBGD-deficient and control mice

	PBGD activity (pkat/g protein) (mean ± SD)
Tissue	PBGD-deficient mice (n = 12)	Control mice (n = 11)	% of control
Blood cells	36.7 ± 19.7	126 ± 72.6	29
Lung	35.4 ± 3.3	85 ± 14.7	42
Kidney	29.9 ± 6.2	91.5 ± 6.4	33
Heart	29.9 ± 2.2	78.6 ± 7.2	38
Brain	18.1 ± 3.6	64.7 ± 7.5	28
Muscle	13.4 ± 3.6	39.2 ± 1.6	34
Spleen	142 ± 195	644 ± 430	22