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. 1987 Nov;28(11):1531–1547. doi: 10.1136/gut.28.11.1531

Cystic fibrosis--a gastroenterological cornucopia.

P L Zentler-Munro 1
PMCID: PMC1433695  PMID: 3322958

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

  1. Abrams C. K., Hamosh M., Dutta S. K., Hubbard V. S., Hamosh P. Role of nonpancreatic lipolytic activity in exocrine pancreatic insufficiency. Gastroenterology. 1987 Jan;92(1):125–129. doi: 10.1016/0016-5085(87)90848-1. [DOI] [PubMed] [Google Scholar]
  2. Abrams C. K., Hamosh M., Hubbard V. S., Dutta S. K., Hamosh P. Lingual lipase in cystic fibrosis. Quantitation of enzyme activity in the upper small intestine of patients with exocrine pancreatic insufficiency. J Clin Invest. 1984 Feb;73(2):374–382. doi: 10.1172/JCI111222. [DOI] [PMC free article] [PubMed] [Google Scholar]
  3. Adrian T. E., McKiernan J., Johnstone D. I., Hiller E. J., Vyas H., Sarson D. L., Bloom S. R. Hormonal abnormalities of the pancreas and gut in cystic fibrosis. Gastroenterology. 1980 Sep;79(3):460–465. [PubMed] [Google Scholar]
  4. Allen J. M., Penketh A. R., Adrian T. E., Lee Y. C., Sarson D. L., Hodson M. E., Batten J. C., Bloom S. R. Adult cystic fibrosis: postprandial response of gut regulatory peptides. Gastroenterology. 1983 Dec;85(6):1379–1383. [PubMed] [Google Scholar]
  5. Anderson C. M. Hypothesis revisited: cystic fibrosis: a disturbance of water and electrolyte movement in exocrine secretory tissue associated with altered prostaglandin (PGE2) metabolism? J Pediatr Gastroenterol Nutr. 1984;3(1):15–22. [PubMed] [Google Scholar]
  6. Bali A., Stableforth D. E., Asquith P. Prolonged small-intestinal transit time in cystic fibrosis. Br Med J (Clin Res Ed) 1983 Oct 8;287(6398):1011–1013. doi: 10.1136/bmj.287.6398.1011. [DOI] [PMC free article] [PubMed] [Google Scholar]
  7. Bank S., Marks I. N., Novis B. Sweat electrolytes in chronic pancreatitis. Am J Dig Dis. 1978 Feb;23(2):178–181. doi: 10.1007/BF01073197. [DOI] [PubMed] [Google Scholar]
  8. Berg N. O., Dahlqvist A., Lindberg T. Exocrine pancreatic insufficiency, small intestinal dysfunction and protein intolerance. A chance occurrence or a connection? Acta Paediatr Scand. 1979 Mar;68(2):275–276. doi: 10.1111/j.1651-2227.1979.tb05002.x. [DOI] [PubMed] [Google Scholar]
  9. Beverley D. W., Kelleher J., MacDonald A., Littlewood J. M., Robinson T., Walters M. P. Comparison of four pancreatic extracts in cystic fibrosis. Arch Dis Child. 1987 Jun;62(6):564–568. doi: 10.1136/adc.62.6.564. [DOI] [PMC free article] [PubMed] [Google Scholar]
  10. Boland M. P., Stoski D. S., MacDonald N. E., Soucy P., Patrick J. Chronic jejunostomy feeding with a non-elemental formula in undernourished patients with cystic fibrosis. Lancet. 1986 Feb 1;1(8475):232–234. doi: 10.1016/s0140-6736(86)90772-5. [DOI] [PubMed] [Google Scholar]
  11. Boyle B. J., Long W. B., Balistreri W. F., Widzer S. J., Huang N. Effect of cimetidine and pancreatic enzymes on serum and fecal bile acids and fat absorption in cystic fibrosis. Gastroenterology. 1980 May;78(5 Pt 1):950–953. [PubMed] [Google Scholar]
  12. Bye A. M., Muller D. P., Wilson J., Wright V. M., Mearns M. B. Symptomatic vitamin E deficiency in cystic fibrosis. Arch Dis Child. 1985 Feb;60(2):162–164. doi: 10.1136/adc.60.2.162-a. [DOI] [PMC free article] [PubMed] [Google Scholar]
  13. Campbell I. M., Crozier D. N., Caton R. B. Abnormal fatty acid composition and impaired oxygen supply in cystic fibrosis patients. Pediatrics. 1976 Apr;57(4):480–486. [PubMed] [Google Scholar]
  14. Chalmers D. M., Brown R. C., Miller M. G., Clarke P. C., Kelleher J., Littlewood J. M., Losowsky M. S. The influence of long-term cimetidine as an adjuvant to pancreatic enzyme therapy in cystic fibrosis. Acta Paediatr Scand. 1985 Jan;74(1):114–117. doi: 10.1111/j.1651-2227.1985.tb10930.x. [DOI] [PubMed] [Google Scholar]
  15. Chase H. P., Dupont J. Abnormal levels of prostaglandins and fatty acids in blood of children with cystic fibrosis. Lancet. 1978 Jul 29;2(8083):236–238. doi: 10.1016/s0140-6736(78)91746-4. [DOI] [PubMed] [Google Scholar]
  16. Chase H. P., Long M. A., Lavin M. H. Cystic fibrosis and malnutrition. J Pediatr. 1979 Sep;95(3):337–347. doi: 10.1016/s0022-3476(79)80504-1. [DOI] [PubMed] [Google Scholar]
  17. Cleghorn G. J., Stringer D. A., Forstner G. G., Durie P. R. Treatment of distal intestinal obstruction syndrome in cystic fibrosis with a balanced intestinal lavage solution. Lancet. 1986 Jan 4;1(8471):8–11. doi: 10.1016/s0140-6736(86)91894-5. [DOI] [PubMed] [Google Scholar]
  18. Colombo C., Roda A., Roda E., Piceni Sereni L., Brega A., Fugazza R., Giunta A. Bile acid malabsorption in cystic fibrosis with and without pancreatic insufficiency. J Pediatr Gastroenterol Nutr. 1984 Sep;3(4):556–562. doi: 10.1097/00005176-198409000-00014. [DOI] [PubMed] [Google Scholar]
  19. Colombo C., Roda A., Roda E., Piceni Sereni L., Maspero D., Giunta A. M., Barbara L. Evaluation of an oral ursodeoxycholic acid load in the assessment of bile acid malabsorption in cystic fibrosis. Dig Dis Sci. 1983 Apr;28(4):306–311. doi: 10.1007/BF01324946. [DOI] [PubMed] [Google Scholar]
  20. Congden P. J., Bruce G., Rothburn M. M., Clarke P. C., Littlewood J. M., Kelleher J., Losowsky M. S. Vitamin status in treated patients with cystic fibrosis. Arch Dis Child. 1981 Sep;56(9):708–714. doi: 10.1136/adc.56.9.708. [DOI] [PMC free article] [PubMed] [Google Scholar]
  21. Cox K. L., Isenberg J. N., Ament M. E. Gastric acid hypersecretion in cystic fibrosis. J Pediatr Gastroenterol Nutr. 1982;1(4):559–565. doi: 10.1097/00005176-198212000-00019. [DOI] [PubMed] [Google Scholar]
  22. Cox K. L., Isenberg J. N., Osher A. B., Dooley R. R. The effect of cimetidine on maldigestion in cystic fibrosis. J Pediatr. 1979 Mar;94(3):488–492. doi: 10.1016/s0022-3476(79)80609-5. [DOI] [PubMed] [Google Scholar]
  23. Darling P. B., Lepage G., Leroy C., Masson P., Roy C. C. Effect of taurine supplements on fat absorption in cystic fibrosis. Pediatr Res. 1985 Jun;19(6):578–582. doi: 10.1203/00006450-198506000-00015. [DOI] [PubMed] [Google Scholar]
  24. Davidson G. P., Hassel F. M., Crozier D., Corey M., Forstner G. G. Iatrogenic hyperuricemia in children with cystic fibrosis. J Pediatr. 1978 Dec;93(6):976–978. doi: 10.1016/s0022-3476(78)81225-6. [DOI] [PubMed] [Google Scholar]
  25. Durie P. R., Bell L., Linton W., Corey M. L., Forstner G. G. Effect of cimetidine and sodium bicarbonate on pancreatic replacement therapy in cystic fibrosis. Gut. 1980 Sep;21(9):778–786. doi: 10.1136/gut.21.9.778. [DOI] [PMC free article] [PubMed] [Google Scholar]
  26. Dutta S. K., Rubin J., Harvey J. Comparative evaluation of the therapeutic efficacy of a pH-sensitive enteric coated pancreatic enzyme preparation with conventional pancreatic enzyme therapy in the treatment of exocrine pancreatic insufficiency. Gastroenterology. 1983 Mar;84(3):476–482. [PubMed] [Google Scholar]
  27. Farrell P. M., Mischler E. H., Engle M. J., Brown D. J., Lau S. M. Fatty acid abnormalities in cystic fibrosis. Pediatr Res. 1985 Jan;19(1):104–109. doi: 10.1203/00006450-198501000-00028. [DOI] [PubMed] [Google Scholar]
  28. Fondacaro J. D., Heubi J. E., Kellogg F. W. Intestinal bile acid malabsorption in cystic fibrosis: a primary mucosal cell defect. Pediatr Res. 1982 Jun;16(6):494–498. doi: 10.1203/00006450-198206000-00019. [DOI] [PubMed] [Google Scholar]
  29. Frase L. L., Strickland A. D., Kachel G. W., Krejs G. J. Enhanced glucose absorption in the jejunum of patients with cystic fibrosis. Gastroenterology. 1985 Feb;88(2):478–484. doi: 10.1016/0016-5085(85)90510-4. [DOI] [PubMed] [Google Scholar]
  30. Friedman H. Z., Langman C. B., Favus M. J. Vitamin D metabolism and osteomalacia in cystic fibrosis. Gastroenterology. 1985 Mar;88(3):808–813. doi: 10.1016/0016-5085(85)90156-8. [DOI] [PubMed] [Google Scholar]
  31. Gaskin K. J., Durie P. R., Corey M., Wei P., Forstner G. G. Evidence for a primary defect of pancreatic HCO3-secretion in cystic fibrosis. Pediatr Res. 1982 Jul;16(7):554–557. doi: 10.1203/00006450-198207000-00012. [DOI] [PubMed] [Google Scholar]
  32. Gaskin K. J., Durie P. R., Lee L., Hill R., Forstner G. G. Colipase and lipase secretion in childhood-onset pancreatic insufficiency. Delineation of patients with steatorrhea secondary to relative colipase deficiency. Gastroenterology. 1984 Jan;86(1):1–7. [PubMed] [Google Scholar]
  33. Gaskin K., Gurwitz D., Durie P., Corey M., Levison H., Forstner G. Improved respiratory prognosis in patients with cystic fibrosis with normal fat absorption. J Pediatr. 1982 Jun;100(6):857–862. doi: 10.1016/s0022-3476(82)80501-5. [DOI] [PubMed] [Google Scholar]
  34. Goodchild M. C., Murphy G. M., Howell A. M., Nutter S. A., Anderson C. M. Aspects of bile acid metabolism in cystic fibrosis. Arch Dis Child. 1975 Oct;50(10):769–778. doi: 10.1136/adc.50.10.769. [DOI] [PMC free article] [PubMed] [Google Scholar]
  35. Gow R., Bradbear R., Francis P., Shepherd R. Comparative study of varying regimens to improve steatorrhoea and creatorrhoea in cystic fibrosis: Effectiveness of an enteric-coated preparation with and without antacids and cimetidine. Lancet. 1981 Nov 14;2(8255):1071–1074. doi: 10.1016/s0140-6736(81)91276-9. [DOI] [PubMed] [Google Scholar]
  36. Graham D. Y. An enteric-coated pancreatic enzyme preparation that works. Dig Dis Sci. 1979 Dec;24(12):906–909. doi: 10.1007/BF01311943. [DOI] [PubMed] [Google Scholar]
  37. Graham D. Y. Pancreatic enzyme replacement: the effect of antacids or cimetidine. Dig Dis Sci. 1982 Jun;27(6):485–490. doi: 10.1007/BF01296725. [DOI] [PubMed] [Google Scholar]
  38. Graham N., Manhire A. R., Stead R. J., Lees W. R., Hodson M. E., Batten J. C. Cystic fibrosis: ultrasonographic findings in the pancreas and hepatobiliary system correlated with clinical data and pathology. Clin Radiol. 1985 Mar;36(2):199–203. doi: 10.1016/s0009-9260(85)80120-3. [DOI] [PubMed] [Google Scholar]
  39. Hadorn B., Johansen P. G., Anderson C. M. Pancreozymin secretin test of exocrine pancreatic funtion in cystic fribrosis and the significance of the result for the pathogenesis of the disease. Can Med Assoc J. 1968 Feb 24;98(8):377–385. [PMC free article] [PubMed] [Google Scholar]
  40. Hanly J. G., Fitzgerald M. X. Meconium ileus equivalent in older patients with cystic fibrosis. Br Med J (Clin Res Ed) 1983 Apr 30;286(6375):1411–1413. doi: 10.1136/bmj.286.6375.1411. [DOI] [PMC free article] [PubMed] [Google Scholar]
  41. Harries J. T., Muller D. P., McCollum J. P., Lipson A., Roma E., Norman A. P. Intestinal bile salts in cystic fibrosis: studies in the patient and experimental animal. Arch Dis Child. 1979 Jan;54(1):19–24. doi: 10.1136/adc.54.1.19. [DOI] [PMC free article] [PubMed] [Google Scholar]
  42. Hernanz-Schulman M., Kirkpatrick J., Jr, Shwachman H., Herman T., Schulman G., Vawter G. F. Pneumatosis intestinalis in cystic fibrosis. Radiology. 1986 Aug;160(2):497–499. doi: 10.1148/radiology.160.2.3726132. [DOI] [PubMed] [Google Scholar]
  43. Hodges P., Sauriol D., Man S. F., Reichert A., Grace M., Talbot T. W., Brown N., Thomson A. B. Nutrient intake of patients with cystic fibrosis. J Am Diet Assoc. 1984 Jun;84(6):664–669. [PubMed] [Google Scholar]
  44. Hodson M. E., Mearns M. B., Batten J. C. Meconium ileus equivalent in adults with cystic fibrosis of pancreas: a report of six cases. Br Med J. 1976 Oct 2;2(6039):790–791. doi: 10.1136/bmj.2.6039.790. [DOI] [PMC free article] [PubMed] [Google Scholar]
  45. Holt T. L., Ward L. C., Francis P. J., Isles A., Cooksley W. G., Shepherd R. W. Whole body protein turnover in malnourished cystic fibrosis patients and its relationship to pulmonary disease. Am J Clin Nutr. 1985 May;41(5):1061–1066. doi: 10.1093/ajcn/41.5.1061. [DOI] [PubMed] [Google Scholar]
  46. Hubbard V. S., Mangrum P. J. Energy intake and nutrition counseling in cystic fibrosis. J Am Diet Assoc. 1982 Feb;80(2):127–131. [PubMed] [Google Scholar]
  47. Hubbard V. S. What is the association of essential fatty acid status with cystic fibrosis? Eur J Pediatr. 1983 Dec;141(2):68–70. doi: 10.1007/BF00496792. [DOI] [PubMed] [Google Scholar]
  48. Hubbard V. S., Wolf R. O., Lester L. A., Egge A. C. Diagnostic and therapeutic applications of bentiromide screening test for exocrine pancreatic insufficiency in patients with cystic fibrosis. Comparison with other tests of exocrine pancreatic disease. Dig Dis Sci. 1984 Oct;29(10):881–889. doi: 10.1007/BF01312475. [DOI] [PubMed] [Google Scholar]
  49. Hultcrantz R., Mengarelli S., Strandvik B. Morphological findings in the liver of children with cystic fibrosis: a light and electron microscopical study. Hepatology. 1986 Sep-Oct;6(5):881–889. doi: 10.1002/hep.1840060513. [DOI] [PubMed] [Google Scholar]
  50. Imrie J. R., Fagan D. G., Sturgess J. M. Quantitative evaluation of the development of the exocrine pancreas in cystic fibrosis and control infants. Am J Pathol. 1979 Jun;95(3):697–708. [PMC free article] [PubMed] [Google Scholar]
  51. Isenberg J. N. Cystic fibrosis: its influence on the liver, biliary tree, and bile salt metabolism. Semin Liver Dis. 1982 Nov;2(4):302–313. doi: 10.1055/s-2008-1040717. [DOI] [PubMed] [Google Scholar]
  52. Isenberg J. N., Hendrix P. Y., Cox K. L. Effect of short-term cimetidine administration on fecal bile acid losses in cystic fibrosis. J Pediatr Gastroenterol Nutr. 1983;2(3):447–451. doi: 10.1097/00005176-198302030-00009. [DOI] [PubMed] [Google Scholar]
  53. Jeffrey I., Durrans D., Wells M., Fox H. The pathology of meconium ileus equivalent. J Clin Pathol. 1983 Nov;36(11):1292–1297. doi: 10.1136/jcp.36.11.1292. [DOI] [PMC free article] [PubMed] [Google Scholar]
  54. Kelleher J., Goode H. F., Field H. P., Walker B. E., Miller M. G., Littlewood J. M. Essential element nutritional status in cystic fibrosis. Hum Nutr Appl Nutr. 1986 Apr;40(2):79–84. [PubMed] [Google Scholar]
  55. Kopelman H., Durie P., Gaskin K., Weizman Z., Forstner G. Pancreatic fluid secretion and protein hyperconcentration in cystic fibrosis. N Engl J Med. 1985 Feb 7;312(6):329–334. doi: 10.1056/NEJM198502073120601. [DOI] [PubMed] [Google Scholar]
  56. Kraemer R., Rüdeberg A., Hadorn B., Rossi E. Relative underweight in cystic fibrosis and its prognostic value. Acta Paediatr Scand. 1978 Jan;67(1):33–37. doi: 10.1111/j.1651-2227.1978.tb16273.x. [DOI] [PubMed] [Google Scholar]
  57. Kusoffsky E., Strandvik B., Troell S. Prospective study of fatty acid supplementation over 3 years in patients with cystic fibrosis. J Pediatr Gastroenterol Nutr. 1983;2(3):434–438. doi: 10.1097/00005176-198302030-00007. [DOI] [PubMed] [Google Scholar]
  58. Landon C., Kerner J. A., Castillo R., Adams L., Whalen R., Lewiston N. J. Oral correction of essential fatty acid deficiency in cystic fibrosis. JPEN J Parenter Enteral Nutr. 1981 Nov-Dec;5(6):501–504. doi: 10.1177/0148607181005006501. [DOI] [PubMed] [Google Scholar]
  59. Larcher V. F., Macdonald A., Vegnente A., Mowat A. P., Eddleston A. L., Williams R. Antibodies to liver-specific lipoprotein in children with chronic liver disease due to "autoimmune" chronic active hepatitis, cystic fibrosis, and alpha 1-antitrypsin deficiency. J Pediatr Gastroenterol Nutr. 1984 Nov;3(5):728–733. doi: 10.1097/00005176-198411000-00016. [DOI] [PubMed] [Google Scholar]
  60. Leclercq-Foucart J., Forget P., Sodoyez-Goffaux F., Zappitelli A. Intestinal permeability to [51Cr]EDTA in children with cystic fibrosis. J Pediatr Gastroenterol Nutr. 1986 May-Jun;5(3):384–387. doi: 10.1097/00005176-198605000-00008. [DOI] [PubMed] [Google Scholar]
  61. Lefebvre D., Ratelle S., Chartrand L., Roy C. C. Reduced microbial transformation of bile acids in cystic fibrosis. Experientia. 1977 May 15;33(5):616–618. doi: 10.1007/BF01946533. [DOI] [PubMed] [Google Scholar]
  62. Leroy C., Lepage G., Morin C. L., Bertrand J. M., Dufour-Larue O., Roy C. C. Effect of dietary fat and residues on fecal loss of sterols and on their microbial degradation in cystic fibrosis. Dig Dis Sci. 1986 Sep;31(9):911–918. doi: 10.1007/BF01303210. [DOI] [PubMed] [Google Scholar]
  63. Lester L. A., Rothberg R. M., Dawson G., Lopez A. L., Corpuz Z. Supplemental parenteral nutrition in cystic fibrosis. JPEN J Parenter Enteral Nutr. 1986 May-Jun;10(3):289–295. doi: 10.1177/0148607186010003289. [DOI] [PubMed] [Google Scholar]
  64. Levy L. D., Durie P. R., Pencharz P. B., Corey M. L. Effects of long-term nutritional rehabilitation on body composition and clinical status in malnourished children and adolescents with cystic fibrosis. J Pediatr. 1985 Aug;107(2):225–230. doi: 10.1016/s0022-3476(85)80130-x. [DOI] [PubMed] [Google Scholar]
  65. Lindström M., Ljusberg-Wahren H., Larsson K., Borgström B. Aqueous lipid phases of relevance to intestinal fat digestion and absorption. Lipids. 1981 Oct;16(10):749–754. doi: 10.1007/BF02535343. [DOI] [PubMed] [Google Scholar]
  66. Mansell A. L., Andersen J. C., Muttart C. R., Ores C. N., Loeff D. S., Levy J. S., Heird W. C. Short-term pulmonary effects of total parenteral nutrition in children with cystic fibrosis. J Pediatr. 1984 May;104(5):700–705. doi: 10.1016/s0022-3476(84)80947-6. [DOI] [PubMed] [Google Scholar]
  67. McCarthy V. P., Mischler E. H., Hubbard V. S., Chernick M. S., di Sant'Agnese P. A. Appendiceal abscess in cystic fibrosis. A diagnostic challenge. Gastroenterology. 1984 Mar;86(3):564–568. [PubMed] [Google Scholar]
  68. McKenna M. C., Hubbard V. S., Bieri J. G. Linoleic acid absorption from lipid supplements in patients with cystic fibrosis with pancreatic insufficiency and in control subjects. J Pediatr Gastroenterol Nutr. 1985 Feb;4(1):45–51. doi: 10.1097/00005176-198502000-00009. [DOI] [PubMed] [Google Scholar]
  69. Mischler E. H., Parrell S. W., Farrell P. M., Raynor W. J., Lemen R. J. Correction of linoleic acid deficiency in cystic fibrosis. Pediatr Res. 1986 Jan;20(1):36–41. doi: 10.1203/00006450-198601000-00010. [DOI] [PubMed] [Google Scholar]
  70. Mischler E. H., Parrell S., Farrell P. M., Odell G. B. Comparison of effectiveness of pancreatic enzyme preparations in cystic fibrosis. Am J Dis Child. 1982 Dec;136(12):1060–1063. doi: 10.1001/archpedi.1982.03970480026006. [DOI] [PubMed] [Google Scholar]
  71. Mitchell E. A., Wesley A. W., Elliott R. B. The treatment of malabsorption in cystic fibrosis with pancreatic extracts and inhibition of gastric acidity by antacids and cimetidine. Aust Paediatr J. 1981 Jun;17(2):89–92. doi: 10.1111/j.1440-1754.1981.tb01911.x. [DOI] [PubMed] [Google Scholar]
  72. Morin C. L., Roy C. C., Lasalle R., Bonin A. Small bowel mucosal dysfunction in patients with cystic fibrosis. J Pediatr. 1976 Feb;88(2):213–216. doi: 10.1016/s0022-3476(76)80984-5. [DOI] [PubMed] [Google Scholar]
  73. Nassif E. G., Younoszai M. K., Weinberger M. M., Nassif C. M. Comparative effects of antacids, enteric coating, and bile salts on the efficacy of oral pancreatic enzyme therapy in cystic fibrosis. J Pediatr. 1981 Feb;98(2):320–323. doi: 10.1016/s0022-3476(81)80671-3. [DOI] [PubMed] [Google Scholar]
  74. O'Halloran S. M., Gilbert J., McKendrick O. M., Carty H. M., Heaf D. P. Gastrografin in acute meconium ileus equivalent. Arch Dis Child. 1986 Nov;61(11):1128–1130. doi: 10.1136/adc.61.11.1128. [DOI] [PMC free article] [PubMed] [Google Scholar]
  75. O'Loughlin E., Forbes D., Parsons H., Scott B., Cooper D., Gall G. Nutritional rehabilitation of malnourished patients with cystic fibrosis. Am J Clin Nutr. 1986 May;43(5):732–737. doi: 10.1093/ajcn/43.5.732. [DOI] [PubMed] [Google Scholar]
  76. Ojeda V. J., Levitt S., Ryan G., Laurence B. H. Cystic fibrosis, Crohn's colitis, and adult meconium ileus equivalent. Dis Colon Rectum. 1986 Sep;29(9):567–571. doi: 10.1007/BF02554256. [DOI] [PubMed] [Google Scholar]
  77. Park R. W., Grand R. J. Gastrointestinal manifestations of cystic fibrosis: a review. Gastroenterology. 1981 Dec;81(6):1143–1161. [PubMed] [Google Scholar]
  78. Parsons H. G., Beaudry P., Dumas A., Pencharz P. B. Energy needs and growth in children with cystic fibrosis. J Pediatr Gastroenterol Nutr. 1983;2(1):44–49. doi: 10.1097/00005176-198302010-00005. [DOI] [PubMed] [Google Scholar]
  79. Parsons H. G., Beaudry P., Pencharz P. B. The effect of nutritional rehabilitation on whole body protein metabolism of children with cystic fibrosis. Pediatr Res. 1985 Feb;19(2):189–192. doi: 10.1203/00006450-198502000-00008. [DOI] [PubMed] [Google Scholar]
  80. Phelan M. S., Fine D. R., Zentler-Munro P. L., Hodson M. E., Batten J. C., Kerr I. H. Radiographic abnormalities of the duodenum in cystic fibrosis. Clin Radiol. 1983 Sep;34(5):573–577. doi: 10.1016/s0009-9260(83)80168-8. [DOI] [PubMed] [Google Scholar]
  81. Read N. W., McFarlane A., Kinsman R. I., Bates T. E., Blackhall N. W., Farrar G. B., Hall J. C., Moss G., Morris A. P., O'Neill B. Effect of infusion of nutrient solutions into the ileum on gastrointestinal transit and plasma levels of neurotensin and enteroglucagon. Gastroenterology. 1984 Feb;86(2):274–280. [PubMed] [Google Scholar]
  82. Regan P. T., Malagelada J. R., DiMagno E. P., Glanzman S. L., Go V. L. Comparative effects of antacids, cimetidine and enteric coating on the therapeutic response to oral enzymes in severe pancreatic insufficiency. N Engl J Med. 1977 Oct 20;297(16):854–858. doi: 10.1056/NEJM197710202971603. [DOI] [PubMed] [Google Scholar]
  83. Regan P. T., Malagelada J. R., Dimagno E. P., Go V. L. Reduced intraluminal bile acid concentrations and fat maldigestion in pancreatic insufficiency: correction by treatment. Gastroenterology. 1979 Aug;77(2):285–289. [PubMed] [Google Scholar]
  84. Robb T. A., Davidson G. P., Kirubakaran C. Conjugated bile acids in serum and secretions in response to cholecystokinin/secretin stimulation in children with cystic fibrosis. Gut. 1985 Nov;26(11):1246–1256. doi: 10.1136/gut.26.11.1246. [DOI] [PMC free article] [PubMed] [Google Scholar]
  85. Rogiers V., Vercruysse A., Dab I., Baran D. Abnormal fatty acid pattern of the plasma cholesterol ester fraction in cystic fibrosis patients with and without pancreatic insufficiency. Eur J Pediatr. 1983 Oct;141(1):39–42. doi: 10.1007/BF00445666. [DOI] [PubMed] [Google Scholar]
  86. Roller R. J., Kern F. Minimal bile acid malabsorption and normal bile acid breath tests in cystic fibrosis and acquired pancreatic insufficiency. Gastroenterology. 1977 Apr;72(4 Pt 1):661–665. [PubMed] [Google Scholar]
  87. Roy C. C., Delage G., Fontaine A., Robitaille L., Chartrand L., Weber A., Morin C. L. The fecal microflora and bile acids in children with cystic fibrosis. Am J Clin Nutr. 1979 Dec;32(12):2404–2409. doi: 10.1093/ajcn/32.12.2404. [DOI] [PubMed] [Google Scholar]
  88. Roy C. C., Lefebvre D., Bélanger G., Chartrand L., Lepage G., Weber A. The effect of lipids on taurocholate absorption from the rat small intestine. Proc Soc Exp Biol Med. 1979 Jun;161(2):105–110. doi: 10.3181/00379727-161-40500. [DOI] [PubMed] [Google Scholar]
  89. Roy C. C., Roulet M., Lefebvre D., Chartrand L., Lepage G., Fournier L. A. The role of gastric lipolysis on fat absorption and bile acid metabolism in the rat. Lipids. 1979 Sep;14(9):811–815. doi: 10.1007/BF02533520. [DOI] [PubMed] [Google Scholar]
  90. Roy C. C., Weber A. M., Morin C. L., Combes J. C., Nusslé D., Mégevand A., Lasalle R. Abnormal biliary lipid composition in cystic fibrosis. Effect of pancreatic enzymes. N Engl J Med. 1977 Dec 15;297(24):1301–1305. doi: 10.1056/NEJM197712152972401. [DOI] [PubMed] [Google Scholar]
  91. Roy C. C., Weber A. M., Morin C. L., Lepage G., Brisson G., Yousef I., Lasalle R. Hepatobiliary disease in cystic fibrosis: a survey of current issues and concepts. J Pediatr Gastroenterol Nutr. 1982;1(4):469–478. doi: 10.1097/00005176-198212000-00005. [DOI] [PubMed] [Google Scholar]
  92. Schöni M., Kraemer R., Ruedeberg A., Lentze M. J., Mordasini R. C., Riesen W. F., Kläy M. P., Rossi E. Long-term cimetidine in children with cystic fibrosis: a randomized double-blind study. Pediatr Res. 1984 Jan;18(1):66–70. [PubMed] [Google Scholar]
  93. Shepherd R. W., Holt T. L., Thomas B. J., Kay L., Isles A., Francis P. J., Ward L. C. Nutritional rehabilitation in cystic fibrosis: controlled studies of effects on nutritional growth retardation, body protein turnover, and course of pulmonary disease. J Pediatr. 1986 Nov;109(5):788–794. doi: 10.1016/s0022-3476(86)80695-3. [DOI] [PubMed] [Google Scholar]
  94. Shepherd R. W., Thomas B. J., Bennett D., Cooksley W. G., Ward L. C. Changes in body composition and muscle protein degradation during nutritional supplementation in nutritionally growth-retarded children with cystic fibrosis. J Pediatr Gastroenterol Nutr. 1983;2(3):439–446. doi: 10.1097/00005176-198302030-00008. [DOI] [PubMed] [Google Scholar]
  95. Slomiany B. L., Murty V. L., Carter S. R., Slomiany A. Effect of covalently bound fatty acids and associated lipids on the viscosity of gastric mucus glycoprotein in cystic fibrosis. Digestion. 1986;34(4):275–280. doi: 10.1159/000199341. [DOI] [PubMed] [Google Scholar]
  96. Smalley C. A., Brown G. A., Parkes M. E., Tease H., Brookes V., Anderson C. M. Reduction of bile acid loss in cystic fibrosis by dietary means. Arch Dis Child. 1978 Jun;53(6):477–482. doi: 10.1136/adc.53.6.477. [DOI] [PMC free article] [PubMed] [Google Scholar]
  97. Soutter V. L., Kristidis P., Gruca M. A., Gaskin K. J. Chronic undernutrition/growth retardation in cystic fibrosis. Clin Gastroenterol. 1986 Jan;15(1):137–155. [PubMed] [Google Scholar]
  98. Spiller R. C., Trotman I. F., Higgins B. E., Ghatei M. A., Grimble G. K., Lee Y. C., Bloom S. R., Misiewicz J. J., Silk D. B. The ileal brake--inhibition of jejunal motility after ileal fat perfusion in man. Gut. 1984 Apr;25(4):365–374. doi: 10.1136/gut.25.4.365. [DOI] [PMC free article] [PubMed] [Google Scholar]
  99. Staub J. L., Sarles H., Soule J. C., Galmiche J. P., Capron J. P. No effects of cimetidine on the therapeutic response to oral enzymes in severe pancreatic insufficiency. N Engl J Med. 1981 May 28;304(22):1364–1365. doi: 10.1056/NEJM198105283042219. [DOI] [PubMed] [Google Scholar]
  100. Stead R. J., Redington A. N., Hinks L. J., Clayton B. E., Hodson M. E., Batten J. C. Selenium deficiency and possible increased risk of carcinoma in adults with cystic fibrosis. Lancet. 1985 Oct 19;2(8460):862–863. doi: 10.1016/s0140-6736(85)90127-8. [DOI] [PubMed] [Google Scholar]
  101. Stead R. J., Skypala I., Hodson M. E., Batten J. C. Enteric coated microspheres of pancreatin in the treatment of cystic fibrosis: comparison with a standard enteric coated preparation. Thorax. 1987 Jul;42(7):533–537. doi: 10.1136/thx.42.7.533. [DOI] [PMC free article] [PubMed] [Google Scholar]
  102. Stern R. C., Rothstein F. C., Doershuk C. F. Treatment and prognosis of symptomatic gallbladder disease in patients with cystic fibrosis. J Pediatr Gastroenterol Nutr. 1986 Jan;5(1):35–40. doi: 10.1097/00005176-198601000-00007. [DOI] [PubMed] [Google Scholar]
  103. Watkins J. B., Tercyak A. M., Szczepanik P., Klein P. D. Bile salt kinetics in cystic fibrosis: influence of pancreatic enzyme replacement. Gastroenterology. 1977 Nov;73(5):1023–1028. [PubMed] [Google Scholar]
  104. Weizman Z., Durie P. R., Kopelman H. R., Vesely S. M., Forstner G. G. Bile acid secretion in cystic fibrosis: evidence for a defect unrelated to fat malabsorption. Gut. 1986 Sep;27(9):1043–1048. doi: 10.1136/gut.27.9.1043. [DOI] [PMC free article] [PubMed] [Google Scholar]
  105. Weizman Z., Forstner G. G., Gaskin K. J., Kopelman H., Wong S., Durie P. R. Bentiromide test for assessing pancreatic dysfunction using analysis of para-aminobenzoic acid in plasma and urine. Studies in cystic fibrosis and Shwachman's syndrome. Gastroenterology. 1985 Sep;89(3):596–604. doi: 10.1016/0016-5085(85)90456-1. [DOI] [PubMed] [Google Scholar]
  106. Willison H. J., Muller D. P., Matthews S., Jones S., Kriss A., Stead R. J., Hodson M. E., Harding A. E. A study of the relationship between neurological function and serum vitamin E concentrations in patients with cystic fibrosis. J Neurol Neurosurg Psychiatry. 1985 Nov;48(11):1097–1102. doi: 10.1136/jnnp.48.11.1097. [DOI] [PMC free article] [PubMed] [Google Scholar]
  107. Wong L. T., Turtle S., Davidson A. G. Secretin pancreozymin stimulation test and confirmation of the diagnosis of cystic fibrosis. Gut. 1982 Sep;23(9):744–750. doi: 10.1136/gut.23.9.744. [DOI] [PMC free article] [PubMed] [Google Scholar]
  108. Yassa J. G., Prosser R., Dodge J. A. Effects of an artificial diet on growth of patients with cystic fibrosis. Arch Dis Child. 1978 Oct;53(10):777–783. doi: 10.1136/adc.53.10.777. [DOI] [PMC free article] [PubMed] [Google Scholar]
  109. Zentler-Munro P. L., Fine D. R., Batten J. C., Northfield T. C. Effect of cimetidine in pancreatic steatorrhoea. Gut. 1986 Sep;27(9):1106–1107. doi: 10.1136/gut.27.9.1106-a. [DOI] [PMC free article] [PubMed] [Google Scholar]
  110. Zentler-Munro P. L., Fine D. R., Batten J. C., Northfield T. C. Effect of cimetidine on enzyme inactivation, bile acid precipitation, and lipid solubilisation in pancreatic steatorrhoea due to cystic fibrosis. Gut. 1985 Sep;26(9):892–901. doi: 10.1136/gut.26.9.892. [DOI] [PMC free article] [PubMed] [Google Scholar]
  111. Zentler-Munro P. L., Fitzpatrick W. J., Batten J. C., Northfield T. C. Effect of intrajejunal acidity on aqueous phase bile acid and lipid concentrations in pancreatic steatorrhoea due to cystic fibrosis. Gut. 1984 May;25(5):500–507. doi: 10.1136/gut.25.5.500. [DOI] [PMC free article] [PubMed] [Google Scholar]

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