Table 2.
Urinary GAG excretion in Gustm(hE540A·mE536A)Sly mice
| Genotype (n = 8) | mg GAG/g creatinine |
|---|---|
| Gustm(hE540A.mE536A)Sly | 893.5 (823–1050)* |
| Wild-type | 213.5 (0–321.8) |
Doubly tolerant MPS VII mice and wild-type littermates were 3–6 months of age. GAG values represent the means and (ranges).
P < 0.0001.