Table 1.

Patient cohort, data base characteristics, distribution of CFTR mutations, and stratification into different types of bronchial infection in study patients with cystic fibrosis

Patient (from database*)			Follow-up statistic (from database*)
	n	%	number of tests		age ranges covered
all	152		total	1460	6 to 10 y	80%
- males	77	50.7	per child	10 (4–15)	11 to 15 y	71%
- females	75	49.3	per year	83(29–116)	16 to 20 y	39%
CFTR mutation stratification
	n	%
ΔF508(2)	86	56.6	Miscellaneous: numbers in brackets
3905insT/ΔF	13	8.6	ΔF508 and1717-1G>A(4), W1282X(4), 2347delG(3), G524X(2), Q525X(2), N1303K(2), 621+1G>T(1),
R553X/ΔF	10	6.6	2176insC(1), 394delTT(1), 4005+1G-A(1). 420del9(1), E585X(1), G126D(1), G85E(1), R347P(1), 1078delT(1);
Miscellaneous	43	28.3	3905insT and1717-1G>A(1),K710X(1), M1101K(1), Q39X(1), P5L(1), R553X(1); R553X andR553X(1); G542X and T5(3), G542X(1); Q542X and3732delA(2); N1303K and2347delG(1), 2789+5G>A(1); 1199delG andR560S(1).
Stratification into different types of infection
	n	%
free from any	6	3.9
intermittend with various*	34	22.4	* H. influenzae, S. aureus, St. maltofilia
S. aureus	19	12.5
P. aeruginosa	36	23.7
P. aeruginosa combined S. aureus	57	37.5

*Actual number of patients in database: 198

Number of patient under age of 6 years: 13

Number of patients with follow-up data less than 4 annual lung function tests: 23