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Journal of Medical Genetics logoLink to Journal of Medical Genetics
. 1999 Apr;36(4):330–332.

Unusual fan shaped ossification in a female fetus with radiological features of boomerang dysplasia

S Odent 1, P Loget 1, B Le Marec 1, A Delezoide 1, P Maroteaux 1
PMCID: PMC1734353  PMID: 10227404

Abstract

We report on a female fetus of 24 weeks whose clinical and radiological findings were compatible with boomerang dysplasia (BD). However, histopathology was unusual with a lateral fan shaped diaphyseal ossification. This has never been described either in typical atelosteogenesis I (AT-I) or in BD. The purpose of this report is to find out if this condition is a separate lethal bone dysplasia or another histological feature of the nosological group of AT-I and BD. 


Keywords: boomerang dysplasia; atelosteogenesis; lethal chondrodysplasia; lethal dwarfism

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