IF analysis of the dystrophin and DAP complexes in gastrocnemius
muscle. (a) Cryosections of mdx muscle,
at 3 months after treatment with construct AAV-MCK-Δ3849 or
AAV-MCK-Δ3990, were IF-stained with an antibody against dystrophin
(green) and then counterstained for cell nuclei with DAPI (blue).
Photos were taken with a ×4 microscope lens. Note the widespread
minidystrophin expression and peripheral nucleation in a majority of
the myofibers. Also note the extensive central nucleation in
minidystrophin-negative areas. (b) Cryosections of
muscles from 15-week-old normal C57/B10 mice, from mdx
mice treated either with vector AAV-MCK-Δ3849, AAV-MCK-Δ3990, or
AAV-MCK-Δ4173, or from untreated mdx mice were
IF-stained with antibodies for dystrophin (green) and counterstained
with DAPI (blue) for nuclei (DYS + DAPI). Note the lack of central
myonuclei. The consecutive sections also were stained with antibodies
for α-sarcoglycan (α-SG), β-sarcoglycan (β-SG), and
γ-sarcoglycan (γ-SG). Photographs were taken with a ×20 lens.