Table 1.
Current clinical management | ||||||
Anatomical diagnosis | Surgically cured | Surgically corrected | Surgically palliated | Medical | Inoperable | Total |
VSD | 33 | 4 | 2† | 50 | 4† | 93 |
Pulmonary valve disease | 37 | 5 | 0 | 22 | 0 | 64 |
Coarctation of the aorta | 1* | 61 | 0 | 1 | 0 | 63 |
Tetralogy of Fallot | 0 | 54 | 1‡ | 0 | 2 | 57 |
Aortic valve disease (including subaortic stenosis) | 3 | 26 | 0 | 27 | 0 | 56 |
Secundum ASD | 22 | 0 | 2† | 7 | 0 | 31 |
Ostium primum septal defect | 0 | 16 | 0 | 0 | 1† | 17 |
d-TGA with or without VSD | 0 | 0 | 13 | 0 | 0 | 13 |
Complete AVSD | 0 | 4 | 0 | 0 | 6 | 10 |
Tricuspid atresia | 0 | 0 | 9 | 0 | 0 | 9 |
l-TGA with or without VSD | 0 | 0 | 4 | 3 | 1† | 8 |
VSD and ASD | 5 | 0 | 1† | 1 | 0 | 7 |
Pulmonary atresia/VSD | 0 | 0 | 5 | 0 | 2 | 7 |
Ebstein's anomaly | 0 | 5 | 0 | 1 | 0 | 6 |
Marfan's syndrome | 0 | 0 | 0 | 6 | 0 | 6 |
Patent ductus arteriosus | 6 | 0 | 0 | 0 | 0 | 6 |
Partial/total APVD | 4 | 0 | 0 | 0 | 0 | 4 |
Congenital conduction abnormalities | 0 | 2 | 0 | 2 | 0 | 4 |
Isolated mitral valve disease | 0 | 2 | 0 | 2 | 0 | 3 |
Atrial isomerism | 0 | 0 | 3 | 0 | 0 | 3 |
Other (truncus arteriosus, atrioventricular tunnel defect, double inlet left ventricle, dilated cardiomyopathy) | 0 | 0 | 2 | 1 | 1 | 4 |
Total | 111 | 179 | 42 | 122 | 17 | 471 |
APVD, anomalous pulmonary venous drainage; ASD, atrial septal defect; AVSD, atrioventricular septal defect; TGA, transposition of the great arteries; VSD, ventricular septal defect.
*Thoracic vascular ring; †severe pulmonary hypertension; ‡other cardiac malformations.