Figure 2.
ERGs on day 1 (before treatment) and subsequent days as indicated; normal control for comparison at bottom. At presentation, only minimal residual scotopic responses were seen in both eyes. Amplitudes of oscillary potentials were only residual. Responses to a single bright white flash in the dark adapted eye were minimal, with amplitudes of approximately one quarter of normal for a-wave and 1/13 for b-wave in both eyes. Single flash cone responses still had normal a-waves, while b-waves were two thirds of normal in both eyes. The 30 Hz flicker responses were four fifths of normal in right eye and normal in left eye. After 3 days of vitamin A supplementation, scotopic responses improved to one third of normal in both eyes. Ten days after initiation of treatment, all ERG parameters were within normal limits, although amplitudes still increased up to day 22.