Table 2.
Case No | Sex | Eye | Age at diagnosis (months) | Best preoperative visual acuity | PHPV type | Indications for surgery | Surgery | Age at surgery (months) | Sequelae and clinical course | Age at final follow up (months) | Visual acuity atfinal follow up | |
1 | M | RE | 2 | Vague LP | A | C RP | L/V | 4 | 30 | F&F | ||
2 | F | LE | 2 | Vague LP | A/P | C RP | L/V | 3 | Indrawing of ciliary processes, LXT small | 14 | Vague LP | |
3 | M | RE | 3 | Poorly F&F | A/P | C | L | 9 | Post-PHPV noted postoperatively, RET | 8 | Poorly fixes | |
4 | M | RE | 1 | Vague LP | A/P | C G | L | 13 | Glaucoma, trab, RD | 16 | NLP | |
5 | M | LE | 0 | NA | A | C RP | L/V | 0 | 42 | 3/18 Kays | ||
6 | F | RE | 0 | Poorly F&F | A | C RP | L/V | 1 | RXT variable, CL compliance poor | 43 | 1/60 SGSL | |
7 | F | RE | 0 | NA | A/P | C RP | L/V | 1 | Pupil closure, pupilloplasty, RET | 12 | 6/570Teller | |
8 | M | LE | 1 | NA | A/P | C RP | L/V | 1 | RD, CL compliance poor | 116 | LP | |
9 | M | RE | 14 | Poorly F&F | A/P | C RP | L/V | 15 | CL compliance poor, secondary IOL | 25 | 6/48 Teller | |
10 | F | LE | 2 | NA | A/P | C | L | 2 | RET | 107 | 6/48 Snellen | |
11 | F | RE | 10 | Poorly F&F | A/P | C RP | L/V | 10 | Pupil closure, pupilloplasty, RET | 42 | LP | |
12 | M | LE | 2 | No F&F | A/P | C RP | L/V | 2 | Phthisis | 23 | Prosthesis | |
13 | M | LE | 4 | No F&F | A/P | C RP AC | L/V | 4 | Glaucoma, phthisis | 22 | NLP | |
14 | M | LE | 1 | Poorly F&F | A/P | C | L | 2 | LET small | 32 | 6/36 Teller | |
15 | M | RE | 0 | Poorly F&F | A | C RP | L/V | 2 | RXT | 1 | F&F | |
16 | F | LE | 4 | 6/480 Teller | A/P | C RP | L/V | 5 | LET, squint surgery | 95 | 3/36 Snellen | |
17 | F | LE | 2 | NA | A | C | L | 2 | LXT, CL compliance poor, secondary IOL | 54 | 3/36 Kays | |
18 | M | LE | 0 | Poorly F&F | A | C RP | L/V | 4 | LXT, enucleation | 20 | NLP | |
19 | M | RE | 1 | NA | A | C RP | L/V | 1 | YAG laser capsulotomy | 22 | 6/36 Teller | |
20 | F | LE | 7 | Poorly F&F | A/P | C | L | 6 | LET, CL compliance poor | 123 | LP | |
21 | M | LE | 2 | NA | A/P | C | L | 6 | LET, squint surgery, threshold ROP, cryotherapy, glaucoma | 17 | 1.5/60 Teller | |
22 | F | LE | 4 | NA | A/P | C RP | L/V | 4 | LET variable | 1 | NA | |
23 | M | RE | 1 | NA | A/P | C RP AC | L/V | 1 | Glaucoma, photocycloablation | 28 | NLP | |
24 | M | RE | 0 | NA | A | C | L | 1 | RET, squint surgery, capsulotomy | 13 | NLP | |
25 | M | LE | 0 | 6/240 Teller | A/P | C | L | 10 | RET, RD | 44 | NLP | |
26 | F | RE | 3 | NA | A | C RP | L/V | 5 | RHT/XT, squint surgery | 104 | NA | |
27 | M | LE | 0 | NA | A/P | C | L | 1 | Dead (PUO) at age 14 months | 8 | 6/120 Teller | |
28R | F | RE | 0 | NA | A/P | G | Trab. | NA | Presented with glaucoma | 8 | NLP | |
28L | F | LE | 0 | NA | A/P | G | Trab. | NA | Presented with glaucoma | 8 | NLP | |
29L | F | LE | 1 | Poorly F&F | A/P | C RP | L/V | 1 | AET, squint surgery | 52 | 1/18 SGSL | |
29R | F | RE | 1 | Poorly F&F | A/P | C RP | L/V | 1 | AET, squint surgery, glaucoma, trab age 4 | 52 | 1/24 SGSL | |
30R | F | RE | 2 | NA | A/P | C RP | L/V | 4 | RD, phthisis, enucleation | 80 | NLP | |
31L | F | LE | 1 | LP | A | C | L | 2 | 63 | 3/24 SGSL |
LP, light perception; NLP, no light perception; F&F, fixing and following; A, anterior PHPV; P, posterior; C, cataract; RP, retrolental plaque; G, glaucoma; AC, shallow anterior chamber; Trab, trabeculectomy; L, lensectomy; V, vitrectomy; RET, right esotropia; LET, left esotropia; RXT, right exotropia; RHT, right hypertropia; AET, alternating esotropia; RD, retinal detachment; ROP, retinopathy of prematurity; CL, contact lens; secondary IOL, secondary intraocular lens; SGSL, Sheridan-Gardner single letters.