Table 3.
Case | Sex | Eye | Age at diagnosis (months) | Visual acuity at presentation | PHPV type | Contraindications to early surgery | Miscellaneous | Age final follow up (months) | Visual acuity at final follow up | |
30L | F | LE | 2 | NLP | A/P | SA SP | Corneal diameter 7 mm, patent hyaloid artery | 80 | NLP | |
31R | F | RE | 1 | LP | A | G SA SP | Glaucoma at presentation, phthisis, prosthesis | 63 | NLP | |
32L | M | LE | 2 | LP | P | SP | Large retrolental mass, smicrocephaly | 2 | LP | |
32R | M | RE | 2 | Vague LP | P | SP | RD, microcephaly | 2 | Vague LP | |
33 | F | LE | 0 | NLP | A/P | SA SP | Microphthalmos, prosthesis | 95 | NLP | |
34 | F | RE | 2 | Vague LP | A/P | SP | Patent hyaloid artery to disc | 2 | Vague LP | |
35 | M | RE | 0 | NLP | A/P | SA SP | Shallow anterior chamber, AP 14 mm | 1 | NLP | |
36 | M | RE | 0 | NLP | A | SA | Shallow anterior chamber, late lensectomy for glaucoma | 17 | NA | |
37 | F | LE | 5 | Poorly F&F | A/P | SP | Patent hyaloid artery to disc, nystagmus | 47 | 3/60 | |
38 | F | RE | 0 | NA | A/P | SA SP | Ectopia lentis, retinal dysplasia, L-ptosis and duct blockage requiring probing. | 22 | NLP | |
39 | M | RE | 0 | NA | A/P | SA SP | Corneal diameter 8 mm, AP s14 mm | 11 | NLP | |
40 | M | LE | 4 | NA | A/P | SA SP | Corneal diameter 8 mm, AP s13 mm | 3 | NLP | |
41 | M | LE | 1 | LP | P | SP | Hyaloid artery, hypoplastic disc, roving nystagmus, microcephaly | 9 | LP | |
42 | M | LE | 0 | NA | P | SP | Progressive phthisis, enucleation | 37 | NLP | |
43 | M | LE | 3 | Good F&F | P | MP | Hyaloid artery only, developmental delay | 11 | 6/18 | |
44 | M | LE | 3 | NA | A | SA | Shallow anterior chamber with pupil bound down | 3 | NLP | |
45 | F | RE | NA | NA | A | SA | Prosthesis | 13 | NLP | |
46 | M | LE | 0 | Poorly F&F | A/P | SA SP | Retrolental mass, AP 12 mm and left ptosis, roving nystagmus | 56 | LP | |
47 | M | LE | 8 | NA | A | SP | Retrolental mass | 8 | NA | |
48 | M | RE | 1 | Roving | P | SP | Vitreous haemorrhage, RD | 14 | NLP | |
49 | M | LE | 4 | NA | P | SP | Hyaloid artery and retrolental mass, | 9 | NLP | |
50 | M | RE | 2 | Poorly F&F | A/P | SA | Shallow anterior chamber, strabismus surgery | 59 | NLP |
LP, light perception; NLP, no light perception; F&F, fixing and following; A, anterior PHPV; P, posterior; MP, minimal posterior PHPV; SP, severe posterior PHPV not amenable to surgery; SA, severe anterior PHPV not amenable to surgery; G, glaucoma; RD, retinal detachment; AP, globe anteroposterior diameter; MRI, magnetic resonance imaging.