Table 1.

 Clinical and histological features of our present case and cases in the literature

	Sex/age (y)	Histological features	Treatment	Evolution	True lymphocytic intestinal leiomyositis
Present case	F 16	T lymphocytic infiltrate in muscularis propria	Steroids and later budesonide. Azathioprine	Mild symptoms, oral nutrition 2 y later	Yes
Nezelof5	M 6 mo	Mononuclear infiltrate in muscularis propria	Steroids	Death 4 y later	Yes
Ruuska6	M 2	Predominant T lymphocytic infiltrate	Steroids, azathioprine, ciclosporin	Total PN	Yes
Mann7	M 47	Chronic inflammatory infiltrate + fibrosis of longitudinal muscle	NR	Death 2 y later	Probably yes
Rigby3	F 27	Predominant fibrosis of the circular layer	Immunosuppression	Oral diet plus gastrostomy feeds. Alive at 21 months	Probably no
Giniès4	F 6 mo	Very polymorphic infiltrate: lymphocytes, plasmocytes, histiocytes, and eosinophils	Steroids	Oral nutrition. Normal weight and height	No (probably B lymphocytes)
McDonald1 cases 1/2/3/4	F 51/F 21/ F 29/F 18	Mucosa predominantly affected	Cyclophosphamide and steroids/steroids/ antibiotics/cisapride	Mild symptoms at 9 y/PN one year later/NR/NR	Probably no (B lymphocytes)
Arista-Nasr2 cases 1/2/3	F 23/F 29/ F 23	Mucosa predominantly affected	Cyclophosphamide/ tetracycline, tinidazol, PE/tetracycline, steroids, chemotherapy.	Death from inanition/death from inanition/alive, severe inanition	Probably no (B lymphocytes)

M, male; F, female; NR, not reported; PN, parenteral nutrition; PE, pancreatic enzymes.