Table 1 Summary of patients with systemic vasculitis who also had a definite (Sapporo criteria) diagnosis of antiphospholipid syndrome.
1 | 64 | M | Polyarteritis nodosa | IgA >160 U/ml multiple occasions | – | Multiple venous thrombotic events | Lifelong warfarin |
2 | 52 | F | Relapsing polychondritis | IgG >16 U/ml multiple occasions | – | Bilateral deep vein thromboses (no other cause found) | Lifelong warfarin |
3 | 56 | M | Wegener's granulomatosis | IgM up to 70 IU/ml multiple occasions | – | DVT × 1 (no other cause found) | Lifelong warfarin |
4 | 56 | F | Churg‐Strauss syndrome | – | Multiple positives | Thrombotic CVA (no other cause found) | Lifelong warfarin |
5 | 64 | M | Unclassified systemic disease | IgG × 2 | – | DVT and PE | Started warfarin, died on ITU |
6 | 71 | F | Giant cell arteritis (29 μ/ml, 17 μ/ml) | IgM × 2 | – | Thrombotic CVA | Lifelong warfarin |
7 | 60 | F | Churg‐Strauss syndrome | – | Multiple positives | Thrombotic CVA | Lifelong warfarin |
8 | 55 | M | Limited Wegener's granulomatosis | IgM > 17 U/ml | – | Thrombotic microangiopathy on renal biopsy | |
9 | 39 | F | Takayasu's disease | IgG 10.4 U/ml | Multiple positives | recurrent abortions (4) and one intrauterine death | Aspirin 75 mg daily |
DVT, deep vein thrombosis; CVA, cardiovascular accident; PE, pulmonary embolism.