Table 1.

Demographic data and lymphocyte subsets of patients with ataxia telangiectasia; major lymphocyte subsets analysed by fluorescence activated cell sorter; values are given as cell counts/µl. Normal values are expressed as ranges, according to values obtained by Shearer et al. [42].

Patient no.	Age/sex (years)	Leucocytes (cells/μl)	Lymphocytes (cells/μl)	CD19+	CD3– CD16+CD56+	CD3+	CD3+/CD4+	CD3+/CD8+	CD4+/ CD45RA+	CD4+/ CD45RO+	CD8+/ CD45RA+	CD8+/ CD45RO+
1	2/m	4 220	945	153	159	575	302	192	n.d.	n.d.	n.d.	n.d.
2	7/f	6 560	1692	256	664	810	552	249	148	485	94	180
3	11/m	4 430	1418	116	554	748	343	311	58	920	78	273
4	11/m	6 400	1184	83	322	750	423	350	37	411	240	239
5	13/f	7 200	1275	64	812	1058	676	412	280	1249	151	261
6	14/f	7 800	2652	203	865	1585	671	724	133	552	151	644
7	14/f	5 300	1590	63	135	994	472	483	116	381	n.d.	n.d.
8	14/m	5 200	1825	66	895	845	264	515	29	252	162	444
9	19/m	1 080	2700	60	550	1110	671	1036	50	636	93	389
10	20/m	16 200	1490	139	253	987	304	630	5	301	n.d.	n.d.
Normal	Under 6	5 500–15 000	> 1200	390–1400	130–720	1400–3700	700–2200	490–1300	430–1500	220–660	380–1100	90–440
values	6–12	4 500–12 000	> 1200	270–860	100–480	1200–2600	650–1500	370–1100	320–1000	230–630	310–900	70–390
	13–20	4 800–10 800	> 1200	110–570	70–480	1000–2200	530–1300	330–920	230–770	240–600	240–710	60–310