Table 1.

VHL-Associated Pancreatic NETs: Patient and Tumor Characteristics

Patient	Age (years) Sex	Procedure	No. of tumors (tumor No.)	Size range (cm)	Location in pancreas	Other pancreatic lesions	Other VHL tumors
1	38F	Partial pancr	1 (1)	3	Body	None	ph, ra
2	48M	Distal pancr; autopsy	5 (2–6)	0.5–2	Head, body, tail	Cysts	h, ra, ph, rcc, rc
3*	34F	Expl. lap with biopsy	2 (7–8)	1.2–8	Head-body	Cysts	h, ra, ph, rcc
4	22M	Partial pancr	2 (9–10)	1–2	Body, tail	Cysts	h, ra, ph, rcc
5	43F	Total pancr	3 (11–13)	2–3	Head, body, tail	Cysts	h, ra, ph, rc
6	23F	Enucleation	3 (14–16)	1.5–4	Head, body, tail	NA	rc
7	29M	Enucleation	1 (17)	2	Tail	Cysts	ph, h, ra, rcc, rc
8	38F	Enucleation	1 (18)	3	Head	NA	rcc
9	39F	Enucleation	1 (19)	1.5	Head	NA	ph
10	42M	Distal pancr	1 (20)	3	Tail	MCA	h
11	42F	Total pancr	1 (21)	0.5	Body-tail	MCA, Carcinoma	h
12	34M	Pancreaticoduod	2 (22–23)	1–2	Head, head	MCA	ph, h, ra, rc
13	18M	Distal pancr	3 (24–26)	0.4–1.5	Tail	None	None
14	35F	Pancreaticoduod and enucleation	4 (27–30)	0.5–1.5	Head, body, tail	None	ra

Abbreviations: F, female; M, male; pancr, pancreatectomy; expl. lap, exploratory laparotomy; pancreaticoduod, pancreaticoduodenectomy (Whipple’s procedure); NA, adjacent pancreas is not available for evaluation; MCA, microcystic adenoma; ph, pheochromocytoma; ra, retinal hemangioma; h, hemangioblastoma; rcc, renal cell carcinoma; rc, renal cysts.

*Patient with liver metastasis (tumor 8).