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. 1998 Nov;153(5):1541–1550. doi: 10.1016/S0002-9440(10)65742-2

Table 2.

Lymph Node Findings in ALPS Patients

Patient Age at Presentation Gender CD95 Mutation Paracortical expansion Follicular hyperplasia Follicular involution PTGC
1 4 months M + + + +
2 18 months F + + + +
3 5 years M + + + +
4 2 years M + + +
5 2 months M + + + +
6 4 months F + + + + +
11 9 months F + + + +
14 9 months F + + +
17 4 months F + + +
20 3 years F + + + +

M, male; F, female.