Table 2.
Lymph Node Findings in ALPS Patients
Patient | Age at Presentation | Gender | CD95 Mutation | Paracortical expansion | Follicular hyperplasia | Follicular involution | PTGC |
---|---|---|---|---|---|---|---|
1 | 4 months | M | + | + | + | − | + |
2 | 18 months | F | + | + | + | + | − |
3 | 5 years | M | + | + | + | − | + |
4 | 2 years | M | + | + | + | − | − |
5 | 2 months | M | + | + | + | − | + |
6 | 4 months | F | + | + | + | + | + |
11 | 9 months | F | − | + | + | + | + |
14 | 9 months | F | − | + | + | − | + |
17 | 4 months | F | + | + | + | − | − |
20 | 3 years | F | + | + | + | + | − |
M, male; F, female.