Table 1 Task force criteria for diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D).
Major criteria | Minor criteria | ||
---|---|---|---|
1 | Global and/or regional dysfunction and structural alterations | Severe RV dilatation and reduction of RVEF with no (or mild) impairment in LVEF | Mild global RV dilatation and/or reduction in RVEF with normal LVEF |
Localised RV aneurysms (dyskinetic areas) | Mild segmental RV dilatation | ||
Severe segmental RV dilatation | Regional RV hypokinesia | ||
2 | Tissue characterisation of walls | Fibrofatty replacement of myocardium on endomyocardial biopsy | |
3 | Repolarisation abnormalities | Inverted T waves in right precordial leads (V2 and V3) (in absence of RBBB) | |
4 | Depolarisation/conduction abnormalities | Epsilon waves or localised prolongation (>110 ms) of the QRS complex in right precordial leads (V1–V3) | Late potentials (signal averaged ECG) |
5 | Arrhythmias | LBBB type (non‐)sustained ventricular tachycardia | |
Frequent ventricular extrasystoles (more than 1000/24 h) | |||
6 | Family history | Familial disease confirmed at necropsy or surgery | Familial history of premature sudden death (<35 years) due to suspected RV dysplasia |
Familial history (clinical diagnosis based on present criteria) |
LBBB, left bundle branch block; LV, left ventricular; LVEF, left ventricular ejection fraction; RBBB, right bundle branch block; RV, right ventricular; RVEF, right ventricular ejection fraction.
Adapted from Furuno et al.13