Table 3 Secondary PH clinical summary.
| Patient | Sex | Age (years) | Diagnosis | Mean PAP (mm Hg) | PVR (units⋅m2) | Treatment duration (months) | WHO class | Six minutes walk | Weight (kg) | |||
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| Baseline | Change | Baseline | % Change | Baseline | % Change | |||||||
| 1 | F | 1.7 | AVSD (E) | 57 | 12 | 22 | III | −1 | 8.7 | 18 | ||
| 2 | M | 2.7 | TGA/Rastelli | 37 | 36.1 | 22 | IV | 0 | 10 | 55 | ||
| 3 | F | 4.2 | AVSD, po | 38 | 4.9 | 16 | III | −1 | 240 | 76 | 15.3 | 16 |
| 4 | F | 4.3 | AVSD, po | – | 20 | 7 | III | 0 | 15 | 11 | ||
| 5 | M | 5.8 | TGA, VSD Switch | 57 | 9.4 | 12 | III | −1 | 110 | 183.5 | 13.4 | 6.7 |
| 6 | F | 10.1 | AVSD (E) | 83 | 36.9 | 17 | III | 0 | 80 | 125 | 27.9 | 12 |
| 7 | F | 11.3 | TA,VSD (E)† | 38 | 18.7 | 11 | IV | −1 | 210 | 24.5 | 18.5 | 19 |
| 8 | M | 14.2 | TAPVD, po | 53 | 13.3 | 19 | IV | −1 | 310 | 36 | 25.8 | 9.26 |
| 9 | M | 14.3 | TGA/Senning | 51 | 8.1 | 18 | III | −1 | 290 | 82 | 59.3 | 17 |
| 10 | M | 15.1 | DORV (E) | 72 | 17.3 | 11 | III | 0 | 80 | 127.5 | 44.1 | 7.5 |
| 11* | F | 15.2 | TGA/Senning | 53 | 18.4 | 16 | IV | −1 | 160 | 187.5 | 42.1 | 7.7 |
| 12 | F | 15.7 | pAVSD, po | 49 | 13.2 | 7 | III | 0 | 400 | 7.5 | 31 | 4.5 |
| 13 | F | 0.6 | CLD | – | – | 2 | IV | 0 | 6.8 | 25 | ||
| 14 | F | 1.9 | CLD | 32 | 10.1 | 19 | III | −1 | 9.3 | 0 | ||
| 15 | M | 2.4 | CLD | 78 | 49 | 12 | III | −1 | 12 | 29 | ||
| 16* | M | 3.3 | Systemic sclerosis + SAH | 43 | 8 | 8 | III | 0 | 9.6 | −6.7 | ||
| 17 | M | 7.3 | Diffuse interstitial lung disease + SAH | 48 | 19.1 | 6 | IV | 0 | 33.5 | 7.2 | ||
| 18 | M | 8.1 | Cutis marmorata | 43 | 8.25 | 5 | III | −1 | 312 | 33.3 | 19.9 | 22.4 |
| 19 | F | 12.25 | CT disorder/pulmonary fibrosis + SAH | – | – | 9 | IV | –1 | 32.8 | 19.6 | ||
| 20 | F | 16 | HIV | 80 | 22.1 | 6 | III | 0 | 340 | −5.8 | 44.4 | 4.95 |
*Taking epoprostenol at start; †repaired truncus arteriosus with interrupted left pulmonary artery and residual ventricular septal defect (VSD).
AVSD, atrioventricular septal defect; CLD, chronic lung disease; CT, connective tissue; DORV, double outlet right ventricle; E, Eisenmenger's syndrome; pAVSD, partial atrioventricular septal defect; po, postoperative; SAH, systemic arterial hypertension; TA, truncus arteriosus; TAPVD, total anomalous pulmonary venous drainage; TGA, transposition of the great arteries.