Table 1.
Brain and CNS nerve sheath tumors and subgroups by site and morphology
| Type of Tumor | ICDO Topography Code | Site | ICDO-2 Histology Code | Histology |
|---|---|---|---|---|
| Nerve sheath tumors | C70.0–C72.9 | Brain, meninges, spinal cord, cranial nerves, and other parts of the CNS | 9540–9570 | Neurofibroma, NOS; neurofibromatosis, NOS; neurofibrosarcoma; melanotic neurofibroma; plexiform neurofibroma; schwannoma, NOS (neurilemmoma, NOS); neurinomatosis; neurilemmoma, malignant; triton tumor, malignant; neuroma, NOS |
| Subgroups of Nerve Sheath Tumors | ||||
| Schwannoma, benign | C70.0–C72.9 | Brain, meninges, spinal cord, cranial nerves, and other parts of the CNS | 9560/0 | Schwannoma, NOS |
| Mutually Exclusive Subgroups of Benign Schwannomas | ||||
| Vestibular schwannoma | C72.4 | Acoustic nerve | 9560/0 | Schwannoma, NOS |
| Nonvestibular schwannoma | C70.0–C72.9, excluding C72.4 | Brain, meninges, spinal cord, cranial nerves (excluding acoustic nerve), and other parts of the CNS | 9560/0 | Schwannoma, NOS |
Abbreviations: ICDO, International Classification of Diseases for Oncology; NOS, not otherwise specified.