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. 2007 Feb 22;175(10):1044–1053. doi: 10.1164/rccm.200610-1483OC

TABLE 2.

CLINICAL CHARACTERISTICS OF THE 48 PATIENTS WITH BIRT-HOGG-DUBÉ SYNDROME WITH PNEUMOTHORAX

Age(s) at Pneumothorax (Treatment)
No. Sex Smoking History No. of Pneumothoraces Right Lung Pneumothorax Left Lung Pneumothorax
1 M N 5 23 (TT), 25 (TT), 25 (TT/TH/MP) 29 (TT), 29 (TH/MP)
2 M Y 1 52 (TT/TH/LR)
3 F Y 1 30 (TT)
4 F N 1 27 (TT)
5 F N 4 24(TT), 28(TT/TH/CP), 38(TT/TH/MP) 26 (TT/TH/MP)
6 F N 2 38 (N), 43 (TT/TH/LR)
7 M Y 4 56 (TT/TH/LR/MP) 43 (TT), 48 (TH/LR/MP), 60 (TT/TH/MP)
8 M N 2 42 (N), 46 (TH/MP)
9 M Y 3 50 (N), 51 (N) 49 (N)
10 F N 1 43 (N)
11 M N 1 45 (TT/TH/LR/MP)
12 F Y 2 34 (N), 38 (TH/MP)
13 M N 1 31 (TT/TH/MP)
14 F N 1 41 (TT)
15 M N 3 39 (TT), 50 (TH/LR), 52 (TH/MP)
16 F N 2 42 (TT), 42 (TT/CP)
17 F Y 1 44 (TT)
18 M N 1 49 (TT/TH/LR)
19 M Y 5 40 (TT), 46 (TT), 52 (TT/CP) 44 (TT), 48 (TH/MP)
20 F Y 1 54 (N)
21 M Y 3 36 (TT), 36 (TT/TH/CP), 38 (TH/MP)
22 M Y 2 35 (TT), 38 (TT)
23 M Y 2 22 (TT), 22 (TT)
24 F N 2 47 (TH/MP) 37 (TT/CP)
25 M N 2 41 (N), 42 (N)
26 F N 2 37 (N), 41 (TT)
27 F N 1 44 (TT)
28 F Y 5 22 (TT/TH/LR), 22 (TT/TH/LR), 22 (TH/LR) 29 (N), 39 (N)
29 M N 1 38 (N)
30 M N 1 27 (N)
31 F N 3 31 (TT), 41 (TT/CP), 42 (TT/CP)
32 M N 1 35(N)
33 F N 2 58 (TT), 58 (TH/MP)
34 F N 1 26 (N)
35 M Y 1 32 (TH/MP) 32 (TH/MP)
36 F N 2 43 (TT), 45 (TT/TH/LR)
37 M N 4 30 (TT), 30 (TH/CP), 30 (TH/CP) 32 (N)
38 F N 1 45 (TT)
39 F Y 1 46 (TT)
40 F N 4 39 (TT), 39 (TT), 39 (TT/TH/MP) 39 (N)
41 F N 1 23 (TT)
42 F Y 5 24 (N), 25 (N), 25 (N), 26 (N), 27 (TT/TH/LR/MP)
43 F N 1 36 (TH/LR)
44 F N 3 50 (TT), 60 (TT/TH/LR/MP) 52 (TT)
45 M N 2 55 (TT), 55 (TH/PM)
46 F Y 2 36 (TT/TH/LR/CP), 36(TT/TH/MP)
47 F N 2 37 (TT), 38 (TT/CP)
48 F N 2 71 (TT), 75 (TT/TH/LR/MP)

Definition of abbreviations: CP = chemical pleurodesis; LR = lung resection; MP = mechanical pleurodesis; N = no treatment; TH = thoracostomy; TT = tube thoracostomy.