TABLE 2.
CLINICAL CHARACTERISTICS OF THE 48 PATIENTS WITH BIRT-HOGG-DUBÉ SYNDROME WITH PNEUMOTHORAX
Age(s) at Pneumothorax (Treatment)
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No. | Sex | Smoking History | No. of Pneumothoraces | Right Lung Pneumothorax | Left Lung Pneumothorax |
1 | M | N | 5 | 23 (TT), 25 (TT), 25 (TT/TH/MP) | 29 (TT), 29 (TH/MP) |
2 | M | Y | 1 | 52 (TT/TH/LR) | |
3 | F | Y | 1 | 30 (TT) | |
4 | F | N | 1 | 27 (TT) | |
5 | F | N | 4 | 24(TT), 28(TT/TH/CP), 38(TT/TH/MP) | 26 (TT/TH/MP) |
6 | F | N | 2 | 38 (N), 43 (TT/TH/LR) | |
7 | M | Y | 4 | 56 (TT/TH/LR/MP) | 43 (TT), 48 (TH/LR/MP), 60 (TT/TH/MP) |
8 | M | N | 2 | 42 (N), 46 (TH/MP) | |
9 | M | Y | 3 | 50 (N), 51 (N) | 49 (N) |
10 | F | N | 1 | 43 (N) | |
11 | M | N | 1 | 45 (TT/TH/LR/MP) | |
12 | F | Y | 2 | 34 (N), 38 (TH/MP) | |
13 | M | N | 1 | 31 (TT/TH/MP) | |
14 | F | N | 1 | 41 (TT) | |
15 | M | N | 3 | 39 (TT), 50 (TH/LR), 52 (TH/MP) | |
16 | F | N | 2 | 42 (TT), 42 (TT/CP) | |
17 | F | Y | 1 | 44 (TT) | |
18 | M | N | 1 | 49 (TT/TH/LR) | |
19 | M | Y | 5 | 40 (TT), 46 (TT), 52 (TT/CP) | 44 (TT), 48 (TH/MP) |
20 | F | Y | 1 | 54 (N) | |
21 | M | Y | 3 | 36 (TT), 36 (TT/TH/CP), 38 (TH/MP) | |
22 | M | Y | 2 | 35 (TT), 38 (TT) | |
23 | M | Y | 2 | 22 (TT), 22 (TT) | |
24 | F | N | 2 | 47 (TH/MP) | 37 (TT/CP) |
25 | M | N | 2 | 41 (N), 42 (N) | |
26 | F | N | 2 | 37 (N), 41 (TT) | |
27 | F | N | 1 | 44 (TT) | |
28 | F | Y | 5 | 22 (TT/TH/LR), 22 (TT/TH/LR), 22 (TH/LR) | 29 (N), 39 (N) |
29 | M | N | 1 | 38 (N) | |
30 | M | N | 1 | 27 (N) | |
31 | F | N | 3 | 31 (TT), 41 (TT/CP), 42 (TT/CP) | |
32 | M | N | 1 | 35(N) | |
33 | F | N | 2 | 58 (TT), 58 (TH/MP) | |
34 | F | N | 1 | 26 (N) | |
35 | M | Y | 1 | 32 (TH/MP) | 32 (TH/MP) |
36 | F | N | 2 | 43 (TT), 45 (TT/TH/LR) | |
37 | M | N | 4 | 30 (TT), 30 (TH/CP), 30 (TH/CP) | 32 (N) |
38 | F | N | 1 | 45 (TT) | |
39 | F | Y | 1 | 46 (TT) | |
40 | F | N | 4 | 39 (TT), 39 (TT), 39 (TT/TH/MP) | 39 (N) |
41 | F | N | 1 | 23 (TT) | |
42 | F | Y | 5 | 24 (N), 25 (N), 25 (N), 26 (N), 27 (TT/TH/LR/MP) | |
43 | F | N | 1 | 36 (TH/LR) | |
44 | F | N | 3 | 50 (TT), 60 (TT/TH/LR/MP) | 52 (TT) |
45 | M | N | 2 | 55 (TT), 55 (TH/PM) | |
46 | F | Y | 2 | 36 (TT/TH/LR/CP), 36(TT/TH/MP) | |
47 | F | N | 2 | 37 (TT), 38 (TT/CP) | |
48 | F | N | 2 | 71 (TT), 75 (TT/TH/LR/MP) |
Definition of abbreviations: CP = chemical pleurodesis; LR = lung resection; MP = mechanical pleurodesis; N = no treatment; TH = thoracostomy; TT = tube thoracostomy.