Table 1.

Clinical characteristics of the study population

	CD	UC	PSC	AIH	WG	mPAN	SLE	Normals
No. (total n = 153)	13	29	34	26	19	12	10	10
Sex (M/F)	9/4	11/18	23/11	8/18	8/11	7/5	3/7	5/5
Median age (years)	36	40	40	41	56	63	41	34
(range)	(17–49)	(10–82)	(12–62)	(9–71)	(33–72)	(56–77)	(26–59)	(21–43)
Concomitant IBDa	–	–	16	0	0	0	0	0
Concomitant PSCb	0	0	–	6	0	0	0	0
ANCA-positive	13	29	34	26	19	12	10	0
ANA-positive	0	1	3	4	0	0	10	0
Active/inactive disease	10/3	25/4	28/6	21/5	12/7	10/2	4/6	0
Immunosuppressionc	7	17	12	18	13	10	5	0

^aAfter initial diagnosis of either PSC or AIH, the patient also developed either ulcerative colitis or Crohn's disease.

^bAfter initial diagnosis of IBD or AIH, the patient also developed PSC.

^cCorticosteroids, azathioprin or cyclosporin A were used for a monotherapy or combined immunosuppressive therapy.