Table 5. .

ETF Fluorescence Reduction Assay of Patient 1 and Control Samples

Sample	Specific Activity (mU/mg)
Liver:
Control	8.6±1.6a
Patient	4.7
VLCAD deficient	5.9b
Fibroblasts:
Control	2.4±0.3a
Patient	2.2
VLCAD deficient	NDc

^aThe SD is derived from the average activities of five normal human liver or cultured skin fibroblast samples.

^bLiterature-reported value.²⁵

^cND = not detectable.