Table 1.
Variable | Mean [SD] | Range | n |
Age (years) | 28.7 [8.4] | 19–52 | 40 |
Age at first menstruation (years) | 12.9 [1.5] | 11–16 | 17 |
Height (cm) | 166.4 [8.4] | 150–183 | 38 |
Weight (kg) | 57.4 [8.0] | 43.3–78 | 38 |
Body mass index (gm / kg2) | 20.6 [2.3] | 16.6–25.1 | 37 |
VO2max (L / min)1 | 1.7 [0.6] | 0.65–2.65 | 37 |
VO2max (% normal) | 87.9 [23.4] | 37–117 | 37 |
FEV1 (L)2 | 1.9 [0.6] | 0.7–3.3 | 37 |
FEV1 (% normal) | 52.3 [15.7] | 22–87 | 37 |
DLCO (mL / min / mmHg)3 | 19.8 [6.5] | 2.05–34.2 | 37 |
DLCO (% normal) | 60.0 [11.6] | 40–85 | 37 |
Exercise capacity (kpm)4 | 797.3 [237.4] | 400–1300 | 37 |
Exercise capacity (% normal) | 76.6 [20.4] | 41–113 | 37 |
Genotype | - | - | |
homozygous Δ F508 | 12 | ||
heterozygous Δ F508 | 18 | ||
other heterozygous | 5 | ||
unknown | 5 |
1 VO2max = oxygen consumption during controlled exercise; 2 FEV1 = forced expiratory volume in one second; 3 DLCO = diffusion of lung (carbon monoxide); 4 exercise capacity = a measure of power output; measured using Stage 1 Jones protocol