Skip to main content
. 2007 May 2;91(10):1311–1314. doi: 10.1136/bjo.2007.116038

Table 1 Ocular and extraocular involvement in juvenile localised scleroderma.

Patient no. Gender Subtype Ocular involvement Ocular findings Extraocular findings
1 F ECDS AA Eyelid abnormalities
2 M ECDS AA Eyelash abnormalities
3 M GM AA Eyelid abnormalities Arthritis
4 M ECDS AA Eyelid–eyelash abnormalities Aortic insufficiency
5 F ECDS AA Eyelid abnormalities Arthritis
6 M ECDS AA Ectropion
7 F ECDS AA Eyelid abnormalities
8 F Linear AA Eyelid abnormalities
9 M GM AA Dry eye
10 F ECDS AA Eyelid abnormalities
11 F ECDS ASI Anterior uveitis
12 F PM ASI Anterior uveitis
13 F ECDS ASI Anterior uveitis
14 M Linear ASI Anterior uveitis, glaucoma Raynaud phenomenon
15 F Linear ASI Anterior uveitis
16 M Linear ASI Episcleritis Peripheral neuropathy
17 F ECDS ASI Episcleritis CNS abnormalities
18 F ECDS CNS‐RA Pupillary mydriasis Epilepsy
19 F ECDS CNS‐RA Pupillary mydriasis, left orbital myositis Pseudotumour cerebri
20 F ECDS CNS‐RA Enophalmos, iris subatrophy, stellar neuroretinitis, retinal teleangieactasiae CNS abnormalities
21 F ECDS M Paralytic strabismus
22 F Linear M Pseudopapilloedema
23 F ECDS M Refractive error Epilepsy
24 M ECDS M Refractive error Abnormal pulmonary function tests

AA, adnexa abnormalities; ASI, anterior segment inflammation; CNS, central nervous system; CNS‐RA, central nervous system‐related abnormalities; ECDS, en coup de sabre; GM, generalised morphea; M, miscellanea; PM, plaque morphea.