Table 1 Ocular and extraocular involvement in juvenile localised scleroderma.
Patient no. | Gender | Subtype | Ocular involvement | Ocular findings | Extraocular findings |
---|---|---|---|---|---|
1 | F | ECDS | AA | Eyelid abnormalities | |
2 | M | ECDS | AA | Eyelash abnormalities | |
3 | M | GM | AA | Eyelid abnormalities | Arthritis |
4 | M | ECDS | AA | Eyelid–eyelash abnormalities | Aortic insufficiency |
5 | F | ECDS | AA | Eyelid abnormalities | Arthritis |
6 | M | ECDS | AA | Ectropion | |
7 | F | ECDS | AA | Eyelid abnormalities | |
8 | F | Linear | AA | Eyelid abnormalities | |
9 | M | GM | AA | Dry eye | |
10 | F | ECDS | AA | Eyelid abnormalities | |
11 | F | ECDS | ASI | Anterior uveitis | |
12 | F | PM | ASI | Anterior uveitis | |
13 | F | ECDS | ASI | Anterior uveitis | |
14 | M | Linear | ASI | Anterior uveitis, glaucoma | Raynaud phenomenon |
15 | F | Linear | ASI | Anterior uveitis | |
16 | M | Linear | ASI | Episcleritis | Peripheral neuropathy |
17 | F | ECDS | ASI | Episcleritis | CNS abnormalities |
18 | F | ECDS | CNS‐RA | Pupillary mydriasis | Epilepsy |
19 | F | ECDS | CNS‐RA | Pupillary mydriasis, left orbital myositis | Pseudotumour cerebri |
20 | F | ECDS | CNS‐RA | Enophalmos, iris subatrophy, stellar neuroretinitis, retinal teleangieactasiae | CNS abnormalities |
21 | F | ECDS | M | Paralytic strabismus | |
22 | F | Linear | M | Pseudopapilloedema | |
23 | F | ECDS | M | Refractive error | Epilepsy |
24 | M | ECDS | M | Refractive error | Abnormal pulmonary function tests |
AA, adnexa abnormalities; ASI, anterior segment inflammation; CNS, central nervous system; CNS‐RA, central nervous system‐related abnormalities; ECDS, en coup de sabre; GM, generalised morphea; M, miscellanea; PM, plaque morphea.