Table 1 Ocular and extraocular involvement in juvenile localised scleroderma.
| Patient no. | Gender | Subtype | Ocular involvement | Ocular findings | Extraocular findings |
|---|---|---|---|---|---|
| 1 | F | ECDS | AA | Eyelid abnormalities | |
| 2 | M | ECDS | AA | Eyelash abnormalities | |
| 3 | M | GM | AA | Eyelid abnormalities | Arthritis |
| 4 | M | ECDS | AA | Eyelid–eyelash abnormalities | Aortic insufficiency |
| 5 | F | ECDS | AA | Eyelid abnormalities | Arthritis |
| 6 | M | ECDS | AA | Ectropion | |
| 7 | F | ECDS | AA | Eyelid abnormalities | |
| 8 | F | Linear | AA | Eyelid abnormalities | |
| 9 | M | GM | AA | Dry eye | |
| 10 | F | ECDS | AA | Eyelid abnormalities | |
| 11 | F | ECDS | ASI | Anterior uveitis | |
| 12 | F | PM | ASI | Anterior uveitis | |
| 13 | F | ECDS | ASI | Anterior uveitis | |
| 14 | M | Linear | ASI | Anterior uveitis, glaucoma | Raynaud phenomenon |
| 15 | F | Linear | ASI | Anterior uveitis | |
| 16 | M | Linear | ASI | Episcleritis | Peripheral neuropathy |
| 17 | F | ECDS | ASI | Episcleritis | CNS abnormalities |
| 18 | F | ECDS | CNS‐RA | Pupillary mydriasis | Epilepsy |
| 19 | F | ECDS | CNS‐RA | Pupillary mydriasis, left orbital myositis | Pseudotumour cerebri |
| 20 | F | ECDS | CNS‐RA | Enophalmos, iris subatrophy, stellar neuroretinitis, retinal teleangieactasiae | CNS abnormalities |
| 21 | F | ECDS | M | Paralytic strabismus | |
| 22 | F | Linear | M | Pseudopapilloedema | |
| 23 | F | ECDS | M | Refractive error | Epilepsy |
| 24 | M | ECDS | M | Refractive error | Abnormal pulmonary function tests |
AA, adnexa abnormalities; ASI, anterior segment inflammation; CNS, central nervous system; CNS‐RA, central nervous system‐related abnormalities; ECDS, en coup de sabre; GM, generalised morphea; M, miscellanea; PM, plaque morphea.