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. 2007 May 2;91(10):1311–1314. doi: 10.1136/bjo.2007.116038

Table 2 Characteristics of patients with and without ocular involvement.

Characteristics Ocular involvement (n = 24) No ocular involvement (n = 726) p (2‐tail)
Gender (F:M) 1.9:1 2.3:1 ns
Age at onset (years, months) <0.05
Mean 5,5 7,4
Median 4,2 7,0
Range 0,2–14,3 0–16,0
JLS subtypes (%)
ECDS 16 (66.7) 97 (13.4) <0.001
Linear 5 (20.8) 373 (51.4) <0.05
Plaque 1 (4.2) 121 (26.3) <0.05
Generalised 2 (8.3) 49 (6.7) ns
Deep 0 (0.0) 16 (2.2) ns
Extraocular involvement (%)
Overall 11 (45.8) 157 (21.6) <0.01
Cardiac 1 (4.2) 1 (0.1) ns
Neurological 6 (25) 28 (3.9) <0.005
Osteoarticular 2 (8.3) 88 (12.1) ns
Respiratory 1 (4.2) 4 (0.5) ns
Vascular 1 (4.2) 17 (2.3) ns
Autoantibodies
ANA positive/tested (%) 12/24 (50.2) 272/648 (42.0) ns
RF positive/tested (%) 2/10 (20.0) 65/398 (16.3) ns
ACL positive/tested (%) 0/5 (0.0) 14/114 (12.3) ns