Table 1 Diagnostic criteria for Adamantiades–Behçet's syndrome (International Study Group for Behçet's Disease, 1990).

Recurrent oral aphthae	At least three times a year (plus any two of the following four criteria)
Genital ulcerations	Active lesion or scar
Skin lesions	Erythema nodosum, foliculitis, other ulcerations
Involvement of the eye	Anterior or posterior uveitis, or retinal vasculitis
Positive pathergy test	Hyper‐reactivity of the skin to pinprick (sterile pustule formed in 24–48 h) – a red papule or pustule >2 mm at the prick site